Disturbed B and T cell homeostasis and neogenesis in patients with ataxia telangiectasia

Journal of Clinical Immunology

Volumn 34, Issue 5, 2014, Pages 561-572

  Kraus, Matan ^a   Lev, Atar ^a   Simon, Amos J ^a   Levran, Inbal ^a   Nissenkorn, Andrea ^a   Levi, Yonit B ^a   Berkun, Yackov ^b   Efrati, Ori ^a   Amariglio, Ninette ^a   Rechavi, Gideon ^a   Somech, Raz ^c,d  

^a SHEBA MEDICAL CENTER   (Israel)

^b HADASSAH HEBREW UNIVERSITY MEDICAL CENTER   (Israel)

^c Edmond and Lily Safra Children's Hospital   (Israel)

^d TEL AVIV UNIVERSITY   (Israel)

Author keywords

Ataxia telangiectasia; ATM; Combined immunodeficiency; Kappa deleting recombination excision circles; KREC; T cell recombination excision circles; TREC

Indexed keywords

ALPHA FETOPROTEIN; ATM PROTEIN; CD20 ANTIGEN; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOGLOBULIN HEAVY CHAIN; IMMUNOGLOBULIN M; ATM PROTEIN, HUMAN; CD3 ANTIGEN; LYMPHOCYTE ANTIGEN RECEPTOR;

ADOLESCENT; ADULT; ANTIBIOTIC PROPHYLAXIS; ARTICLE; ATAXIA TELANGIECTASIA; B LYMPHOCYTE; CD3+ T LYMPHOCYTE; CELL MATURATION; CEREBELLUM ATROPHY; CHILD; CHROMOSOME BREAKAGE; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; FLOW CYTOMETRY; GENE MUTATION; GENE REARRANGEMENT; HOMEOSTASIS; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOGLOBULIN BLOOD LEVEL; ISRAEL; LYMPHOCYTE COUNT; LYMPHOCYTE PROLIFERATION; MALE; MITOGENESIS; NUCLEAR MAGNETIC RESONANCE IMAGING; PERIPHERAL BLOOD MONONUCLEAR CELL; PRIORITY JOURNAL; RECURRENT INFECTION; T LYMPHOCYTE; T LYMPHOCYTE SUBPOPULATION; CELL PROLIFERATION; GENE EXPRESSION; GENETICS; IMMUNOLOGICAL PROCEDURES; IMMUNOLOGY; IMMUNOPHENOTYPING; MUTATION; PATHOLOGY; PRESCHOOL CHILD;

ADOLESCENT; ADULT; ANTIGENS, CD20; ANTIGENS, CD3; ATAXIA TELANGIECTASIA; ATAXIA TELANGIECTASIA MUTATED PROTEINS; B-LYMPHOCYTES; CELL PROLIFERATION; CHILD; CHILD, PRESCHOOL; FEMALE; GENE EXPRESSION; HOMEOSTASIS; HUMANS; IMMUNOLOGIC TESTS; IMMUNOPHENOTYPING; MALE; MUTATION; RECEPTORS, ANTIGEN, B-CELL; RECEPTORS, ANTIGEN, T-CELL; T-LYMPHOCYTE SUBSETS;

EID: 84902375695     PISSN: 02719142     EISSN: 15732592     Source Type: Journal    
DOI: 10.1007/s10875-014-0044-1     Document Type: Article

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