Low thymic output and reduced heterogeneity of alpha/beta, but not gamma/delta, T lymphocytes in infants with ataxia-telangiectasia

Neuropediatrics

Volumn 34, Issue 3, 2003, Pages 165-167

  Micheli, R ^a   Pirovano, S ^b   Calandra, G ^b   Valotti, M ^b   Plebani, A ^c   Albertini, A ^b   Imberti, Luisa ^d,e  

^a Spedali Civili of Brescia   (Italy)

^b UNIVERSITY OF BRESCIA   (Italy)

^c SPEDALI CIVILI   (Italy)

^d Terzo Servizio Analisi   (Italy)

^e Terzo Servizio Analisi   (Italy)

Author keywords

Ataxia telangiectasia; Immunodeficiency; T cell repertoire; TRECs

Indexed keywords

ALPHA FETOPROTEIN; ATM PROTEIN; B LYMPHOCYTE RECEPTOR; DNA; IMMUNOGLOBULIN A; T LYMPHOCYTE RECEPTOR ALPHA CHAIN; T LYMPHOCYTE RECEPTOR BETA CHAIN; T LYMPHOCYTE RECEPTOR DELTA CHAIN; T LYMPHOCYTE RECEPTOR GAMMA CHAIN;

ARTICLE; ATAXIA TELANGIECTASIA; CASE REPORT; GENE MUTATION; GENE REARRANGEMENT; HUMAN; IMMUNE DEFICIENCY; POLYMERASE CHAIN REACTION; PRESCHOOL CHILD; PRIORITY JOURNAL; T LYMPHOCYTE; THYMUS FUNCTION;

ADOLESCENT; ADULT; ATAXIA TELANGIECTASIA; GENE REARRANGEMENT, ALPHA-CHAIN T-CELL ANTIGEN RECEPTOR; GENE REARRANGEMENT, BETA-CHAIN T-CELL ANTIGEN RECEPTOR; GENE REARRANGEMENT, DELTA-CHAIN T-CELL ANTIGEN RECEPTOR; GENE REARRANGEMENT, GAMMA-CHAIN T-CELL ANTIGEN RECEPTOR; GENETIC HETEROGENEITY; HUMANS; INFANT; POINT MUTATION; POLYMERASE CHAIN REACTION; THYMUS GLAND;

EID: 0042734979     PISSN: 0174304X     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2003-41280     Document Type: Article

References (10)

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