Enhanced F508del-CFTR channel activity ameliorates bone pathology in murine cystic fibrosis

American Journal of Pathology

Volumn 184, Issue 4, 2014, Pages 1132-1141

  Le Henaff, Carole ^a   Haÿ, Eric ^b   Velard, Frédéric ^a   Marty, Caroline ^b   Tabary, Olivier ^b   Marie, Pierre J ^b   Jacquot, Jacky P ^a  

^a UNIVERSITÉ DE REIMS CHAMPAGNE ARDENNE   (France)

^b INSERM   (France)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; ESTRADIOL; MIGLUSTAT; SOMATOMEDIN C; 1 DEOXYNOJIRIMYCIN; ENZYME INHIBITOR;

ADULT; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BODY WEIGHT; BONE DENSITY; BONE MASS; CHLORIDE TRANSPORT; CONTROLLED STUDY; CYSTIC FIBROSIS; FEMUR; GENE; HOMOZYGOTE; INDEL MUTATION; LUMBAR SPINE; MOUSE; NONHUMAN; OSSIFICATION; OSTEOBLAST; OSTEOLYSIS; OSTEOPENIA; PHENOTYPE; PRIORITY JOURNAL; TREATMENT DURATION; ANALOGS AND DERIVATIVES; ANIMAL; BONE; CELL CULTURE; COMPLICATION; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR MOUSE; DISEASE MODEL; DRUG EFFECTS; GENETICS; MALE; METABOLISM; MUTATION; PATHOLOGY;

1-DEOXYNOJIRIMYCIN; ANIMALS; BONE AND BONES; CELLS, CULTURED; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DISEASE MODELS, ANIMAL; ENZYME INHIBITORS; MALE; MICE, INBRED CFTR; MUTATION; OSTEOBLASTS;

EID: 84897857417     PISSN: 00029440     EISSN: 15252191     Source Type: Journal    
DOI: 10.1016/j.ajpath.2013.12.027     Document Type: Article

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