C3 dysregulation due to factor H deficiency is mannan-binding lectin-associated serine proteases (MASP)-1 and MASP-3 independent in vivo

Clinical and Experimental Immunology

Volumn 176, Issue 1, 2014, Pages 84-92

  Ruseva, M M ^a   Takahashi, M ^b   Fujita, T ^b   Pickering, M C ^a  

^a IMPERIAL COLLEGE LONDON   (United Kingdom)

^b FUKUSHIMA MEDICAL UNIVERSITY   (Japan)

Author keywords

Complement; Kidney; MASP 1 3

Indexed keywords

COMPLEMENT COMPONENT C3; COMPLEMENT COMPONENT C5; COMPLEMENT FACTOR H; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEINASE; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEINASE 1; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEINASE 3; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BIOACCUMULATION; COMPLEMENT ACTIVATION; COMPLEMENT ALTERNATIVE PATHWAY; COMPLEMENT BLOOD LEVEL; COMPLEMENT DEFICIENCY; COMPLEMENT FACTOR H DEFICIENCY; CONTROLLED STUDY; FEMALE; GLOMERULUS; HEMOLYSIS; IN VIVO STUDY; MOUSE; NONHUMAN; PRIORITY JOURNAL; WESTERN BLOTTING;

COMPLEMENT; KIDNEY; MASP-1/3;

ANIMALS; BLOTTING, WESTERN; COMPLEMENT ACTIVATION; COMPLEMENT C3; COMPLEMENT C5; COMPLEMENT FACTOR B; COMPLEMENT FACTOR D; COMPLEMENT FACTOR H; COMPLEMENT PATHWAY, ALTERNATIVE; ENZYME-LINKED IMMUNOSORBENT ASSAY; GLOMERULAR BASEMENT MEMBRANE; KIDNEY DISEASES; KIDNEY GLOMERULUS; MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT;

EID: 84895552086     PISSN: 00099104     EISSN: 13652249     Source Type: Journal    
DOI: 10.1111/cei.12244     Document Type: Article

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