Interaction of glutaric aciduria type 1-related glutaryl-CoA dehydrogenase with mitochondrial matrix proteins

PLoS ONE

Volumn 9, Issue 2, 2014, Pages

  Schmiesing, Jessica ^a   Schlüter, Hartmut ^a   Ullrich, Kurt ^a   Braulke, Thomas ^a   Mühlhausen, Chris ^a  

^a UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

DIHYDROLIPOAMIDE SUCCINYLTRANSFERASE; ELECTRON TRANSFERRING FLAVOPROTEIN; ELECTRON TRANSFERRING FLAVOPROTEIN BETA SUBUNIT; GLUTARYL COENZYME A DEHYDROGENASE; LYSINE; MITOCHONDRIAL MATRIX PROTEIN; MITOCHONDRIAL PROTEIN; UNCLASSIFIED DRUG; YELLOW FLUORESCENT PROTEIN;

AFFINITY CHROMATOGRAPHY; ANIMAL CELL; ARTICLE; COMPLEX FORMATION; CONTROLLED STUDY; GENETIC COMPLEMENTATION; GLUTARIC ACIDURIA TYPE 1; HUMAN; HUMAN CELL; METABOLIC DISORDER; MITOCHONDRION; NEUROLOGIC DISEASE; NONHUMAN; NUCLEOTIDE SEQUENCE; OLIGOMERIZATION; OXIDATION; PATHOPHYSIOLOGY; PROTEIN ANALYSIS; PROTEIN FUNCTION; PROTEIN ISOLATION; PROTEIN PROTEIN INTERACTION;

ACYLTRANSFERASES; AMINO ACID METABOLISM, INBORN ERRORS; BLOTTING, WESTERN; BRAIN DISEASES, METABOLIC; CHROMATOGRAPHY, AFFINITY; ELECTRON-TRANSFERRING FLAVOPROTEINS; GLUTARATES; GLUTARYL-COA DEHYDROGENASE; HUMANS; IMMUNOPRECIPITATION; MITOCHONDRIAL PROTEINS; RECOMBINANT FUSION PROTEINS;

EID: 84894619896     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0087715     Document Type: Article

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