Kv3.3 channels harbouring a mutation of spinocerebellar ataxia type 13 alter excitability and induce cell death in cultured cerebellar Purkinje cells

Journal of Physiology

Volumn 592, Issue 1, 2014, Pages 229-247

  Irie, Tomohiko ^a,b   Matsuzaki, Yasunori ^b   Sekino, Yuko ^a   Hirai, Hirokazu ^b  

^a NATIONAL INSTITUTE OF HEALTH SCIENCES   (Japan)

^b GUNMA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CALCIUM CHANNEL Q TYPE; CALCIUM ION; GREEN FLUORESCENT PROTEIN; POTASSIUM CHANNEL KV3.3; UNCLASSIFIED DRUG; VOLTAGE GATED POTASSIUM CHANNEL;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; EMBRYO; FEMALE; GENE EXPRESSION; GENE MUTATION; HETEROLOGOUS EXPRESSION; KV3.3 GENE; MALE; MISSENSE MUTATION; MOUSE; NERVE CELL CULTURE; NERVE CELL DIFFERENTIATION; NERVE CELL EXCITABILITY; NERVE CELL NECROSIS; NEUROPATHOLOGY; NEWBORN; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; PURKINJE CELL; SPINOCEREBELLAR DEGENERATION;

ACTION POTENTIALS; ANIMALS; CALCIUM; CALCIUM CHANNEL BLOCKERS; CELL DEATH; CELLS, CULTURED; CEREBELLAR ATAXIA; DENDRITES; MICE; MUTATION, MISSENSE; PURKINJE CELLS; SHAW POTASSIUM CHANNELS; XENOPUS;

EID: 84891372003     PISSN: 00223751     EISSN: 14697793     Source Type: Journal    
DOI: 10.1113/jphysiol.2013.264309     Document Type: Article

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