Platelet hyperreactivity explains the bleeding abnormality and macrothrombocytopenia in a murine model of Sitosterolemia

Blood

Volumn 122, Issue 15, 2013, Pages 2732-2742

  Kanaji, Taisuke ^a   Kanaji, Sachiko ^a   Montgomery, Robert R ^a,b,c   Patel, Shailendra B ^b   Newman, Peter J ^a,b  

^a BLOOD RESEARCH INSTITUTE   (United States)

^b MEDICAL COLLEGE OF WISCONSIN   (United States)

^c Children's Hospital of Wisconsin   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

EZETIMIBE; FIBRINOGEN; FILAMIN; INTEGRIN RECEPTOR; PHYTOSTEROL; SITOSTEROL; VON WILLEBRAND FACTOR;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BLEEDING; CELLULAR DISTRIBUTION; CONTROLLED STUDY; FEMALE; FIBRINOGEN BLOOD LEVEL; HUMAN; INTERNALIZATION; LIPID BLOOD LEVEL; LIPID STORAGE; MOUSE; NONHUMAN; NONSENSE MUTATION; PLATELET MICROPARTICLE; PRIORITY JOURNAL; PROTEIN BINDING; SITOSTEROLEMIA; THROMBOCYTE; THROMBOCYTE ADHESION; THROMBOCYTOPENIA;

EID: 84888251628     PISSN: 00064971     EISSN: 15280020     Source Type: Journal    
DOI: 10.1182/blood-2013-06-510461     Document Type: Article

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