Temperature and drug treatments in mevalonate kinase deficiency: An Ex vivo study

BioMed Research International

Volumn 2013, Issue , 2013, Pages

  Tricarico, Paola Maura ^a   Kleiner, Giulio ^b   Piscianz, Elisa ^b   Zanin, Valentina ^b   Monasta, Lorenzo ^b   Crovella, Sergio ^a,b   Marcuzzi, Annalisa ^b  

^a UNIVERSITY OF TRIESTE   (Italy)

^b INSTITUTE FOR MATERNAL AND CHILD HEALTH IRCCS BURLO GAROFOLO   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

3 HYDROXY 3 METHYLGLUTARYL COENZYME A; EOTAXIN; GAMMA INTERFERON; GAMMA INTERFERON INDUCIBLE PROTEIN 10; GERANIOL; GRANULOCYTE COLONY STIMULATING FACTOR; GRANULOCYTE MACROPHAGE COLONY STIMULATING FACTOR; INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; INTERLEUKIN 10; INTERLEUKIN 12P70; INTERLEUKIN 13; INTERLEUKIN 15; INTERLEUKIN 17; INTERLEUKIN 1ALPHA; INTERLEUKIN 1BETA; INTERLEUKIN 2; INTERLEUKIN 3; INTERLEUKIN 4; INTERLEUKIN 5; INTERLEUKIN 6; INTERLEUKIN 7; INTERLEUKIN 8; INTERLEUKIN 9; LIPOPOLYSACCHARIDE; MEVALONATE KINASE; MONOCYTE CHEMOTACTIC PROTEIN 1; PLATELET DERIVED GROWTH FACTOR BB; RANTES; TIPIFARNIB; VASCULOTROPIN; ANTIINFLAMMATORY AGENT; CARRIER PROTEIN; CYTOKINE; INFLAMMASOME; MEVALONIC ACID; NLRP3 PROTEIN, HUMAN; QUINOLONE DERIVATIVE; TERPENE;

ANTIINFLAMMATORY ACTIVITY; APOPTOSIS; ARTICLE; CASE REPORT; CHILD; CONCENTRATION RESPONSE; CONTROLLED STUDY; ENZYME LINKED IMMUNOSORBENT ASSAY; EX VIVO STUDY; FEMALE; HUMAN; HUMAN CELL; INFLAMMATION; MALE; MEVALONATE KINASE DEFICIENCY; MONOCYTE; PRESCHOOL CHILD; RARE DISEASE; SCHOOL CHILD; TEMPERATURE SENSITIVITY; BIOSYNTHESIS; BLOOD; DRUG EFFECT; METABOLISM; TEMPERATURE; DRUG EFFECTS;

ANTI-INFLAMMATORY AGENTS; APOPTOSIS; BIOSYNTHETIC PATHWAYS; CARRIER PROTEINS; CHILD; CYTOKINES; FEMALE; HUMANS; INFLAMMASOMES; INTERLEUKIN-1BETA; LIPOPOLYSACCHARIDES; MALE; MEVALONATE KINASE DEFICIENCY; MEVALONIC ACID; QUINOLONES; TEMPERATURE; TERPENES;

EID: 84884842222     PISSN: 23146133     EISSN: 23146141     Source Type: Journal    
DOI: 10.1155/2013/715465     Document Type: Article

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