Normal rates of whole-body fat oxidation and gluconeogenesis after overnight fasting and moderate-intensity exercise in patients with medium-chain acyl-CoA dehydrogenase deficiency

Journal of Inherited Metabolic Disease

Volumn 36, Issue 5, 2013, Pages 831-840

  Huidekoper, Hidde H ^a   Ackermans, Mariëtte T ^a   Koopman, René ^b   Van Loon, Luc J C ^b   Sauerwein, Hans P ^a   Wijburg, Frits A ^a,c  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b MAASTRICHT UNIVERSITY MEDICAL CENTER   (Netherlands)

^c ACADEMIC MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

3 HYDROXYBUTYRIC ACID; ACETOACETIC ACID; ADRENALIN; CARNITINE; FATTY ACID; GLUCAGON; GLUCOSE; GLYCOGEN; HYDROCORTISONE; INSULIN; LACTIC ACID; NORADRENALIN; PALMITIC ACID; TRIACYLGLYCEROL;

ADRENALIN BLOOD LEVEL; ADULT; AMINO ACID BLOOD LEVEL; ARTICLE; CLINICAL ARTICLE; CONTROLLED STUDY; CYCLING; DIET RESTRICTION; ENERGY EXPENDITURE; EXERCISE; FATTY ACID BLOOD LEVEL; FATTY ACID OXIDATION; FEMALE; GLUCAGON BLOOD LEVEL; GLUCOSE BLOOD LEVEL; GLUCOSE METABOLISM; HUMAN; HUMAN CELL; HYDROCORTISONE BLOOD LEVEL; INSULIN BLOOD LEVEL; LACTATE BLOOD LEVEL; LIPID METABOLISM; LUNG GAS EXCHANGE; MALE; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE DEFICIENCY; MUSCLE BIOPSY; NORADRENALIN BLOOD LEVEL; REST; SKELETAL MUSCLE;

ACYL-COA DEHYDROGENASE; ADIPOSE TISSUE; ADULT; BLOOD GLUCOSE; ENERGY METABOLISM; EXERCISE; FASTING; FEMALE; GLUCONEOGENESIS; GLUCOSE; GLYCOGEN; HUMANS; LIPID METABOLISM, INBORN ERRORS; MALE; MUSCLE, SKELETAL; OXIDATION-REDUCTION; REST; TRIGLYCERIDES; YOUNG ADULT;

EID: 84884352995     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-012-9532-8     Document Type: Article

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