Safe and unsafe duration of fasting for children with MCAD deficiency

European Journal of Pediatrics

Volumn 166, Issue 1, 2007, Pages 5-11

  Derks, Terry G J ^a   Van Spronsen, Francjan J ^a   Rake, Jan Peter ^b   Van Der Hilst, Christian S ^c   Span, Mark M ^c   Smit, G Peter A ^a  

^a UNIVERSITY OF GRONINGEN   (Netherlands)

^b MARTINI HOSPITAL   (Netherlands)

^c UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

Author keywords

Fasting; Inborn errors of metabolism; Medium chain acyl Coenzyme A dehydrogenase; Neonatal screening; Therapy

Indexed keywords

MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE;

AGE; ARTICLE; CLINICAL ARTICLE; DIET RESTRICTION; ENZYME DEFICIENCY; FEMALE; FEVER; HUMAN; HYPOGLYCEMIA; INBORN ERROR OF METABOLISM; INFANT; MALE; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE DEFICIENCY; NETHERLANDS; NEWBORN SCREENING; PRESCHOOL CHILD; PRIORITY JOURNAL; SAFETY; SYMPTOM; TIME;

ACYL-COA DEHYDROGENASE; CHILD, PRESCHOOL; FASTING; HUMANS; INFANT; METABOLISM, INBORN ERRORS; NETHERLANDS; TIME FACTORS;

EID: 33845425508     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-006-0186-0     Document Type: Article

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