Laforin prevents stress-induced polyglucosan body formation and lafora disease progression in neurons

Molecular Neurobiology

Volumn 48, Issue 1, 2013, Pages 49-61

  Liu, Yan ^a,b   Wang, Yin ^a,b   Ma, Keli ^a   Wang, Peixiang ^c   Baba, Otto ^d   Zhang, Helen ^a   Parent, Jack M ^a   Zheng, Pan ^a   Liu, Yang ^a   Minassian, Berge A ^c  

^a UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

^b GEORGE WASHINGTON UNIVERSITY   (United States)

^c HOSPITAL FOR SICK CHILDREN   (Canada)

^d TOKYO MEDICAL AND DENTAL UNIVERSITY   (Japan)

Author keywords

ER stress; Lafora body; Lafora disease; Laforin; Muscle glycogen synthase; Neurodegeneration; Neuron; Polyglucosan

Indexed keywords

DUAL SPECIFICITY PHOSPHATASE; GLUCOSE 6 PHOSPHATE; GLYCOGEN SYNTHASE; LAFORIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; CELL CULTURE; CONTROLLED STUDY; DISEASE COURSE; ENDOPLASMIC RETICULUM STRESS; ENZYME ACTIVITY; GLYCOGEN ANALYSIS; GLYCOGEN METABOLISM; GLYCOGEN SYNTHESIS; IMMUNOCYTOCHEMISTRY; MOUSE; MYOCLONUS EPILEPSY; NERVE CELL; NERVE CELL CULTURE; NERVE DEGENERATION; NEUROPROTECTION; NONHUMAN; PROTEIN DEPHOSPHORYLATION; PROTEIN PHOSPHORYLATION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; REVIEW; SEIZURE SUSCEPTIBILITY;

EID: 84880876723     PISSN: 08937648     EISSN: 15591182     Source Type: Journal    
DOI: 10.1007/s12035-013-8438-2     Document Type: Review

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