Laforin is required for the functional activation of malin in endoplasmic reticulum stress resistance in neuronal cells

FEBS Journal

Volumn 279, Issue 14, 2012, Pages 2467-2478

  Zeng, Li ^a,b   Wang, Yin ^a   Baba, Otto ^c   Zheng, Pan ^a   Liiu, Yang ^a   Liu, Yan ^a  

^a UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

^b HUAZHONG UNIVERSITY OF SCIENCE AND TECHNOLOGY   (China)

^c TOKYO MEDICAL AND DENTAL UNIVERSITY   (Japan)

Author keywords

endoplasmic reticulum stress; laforin; malin; neuronal cells; polyglucosan

Indexed keywords

GLYCOGEN; LAFORIN; MALIN; MUTANT PROTEIN; PHOSPHATASE; POLYGLUCOSAN; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; APOPTOSIS; ARTICLE; BRAIN NERVE CELL; CELL INCLUSION; CELL NUCLEUS; CONTROLLED STUDY; ENDOPLASMIC RETICULUM STRESS; EPM2A GENE; GENE DELETION; GENE OVEREXPRESSION; GENE SILENCING; MISSENSE MUTATION; MOUSE; MYOCLONUS EPILEPSY; NERVE CELL; NEUROPROTECTION; NHLRC1 GENE; NONHUMAN; POLYGLUCOSAN BODY; POLYUBIQUITINATION; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN EXPRESSION; UBIQUITINATION; WILD TYPE;

ANIMALS; BLOTTING, WESTERN; CELL LINE, TUMOR; DUAL-SPECIFICITY PHOSPHATASES; ENDOPLASMIC RETICULUM STRESS; FEMALE; GLUCANS; HEK293 CELLS; HUMANS; IMMUNOPRECIPITATION; INCLUSION BODIES; LAFORA DISEASE; MALE; MICE; MICE, 129 STRAIN; MICE, INBRED C57BL; MICE, KNOCKOUT; MUTATION; NEURONS; POLYUBIQUITIN; PROTEIN BINDING; UBIQUITIN-PROTEIN LIGASES;

MUS;

EID: 84863454044     PISSN: 1742464X     EISSN: 17424658     Source Type: Journal    
DOI: 10.1111/j.1742-4658.2012.08627.x     Document Type: Article

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