Genetic depletion of the malin e3 ubiquitin ligase in mice leads to Lafora bodies and the accumulation of insoluble laforin

Journal of Biological Chemistry

Volumn 285, Issue 33, 2010, Pages 25372-25381

  DePaoli Roach, Anna A ^a   Tagliabracci, Vincent S ^a   Segvich, Dyann M ^a   Meyer, Catalina M ^a   Irimia, Jose M ^a   Roach, Peter J ^a  

^a INDIANA UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

DEBRANCHING; GLYCOGEN SYNTHASE; LOW SPEED; SKELETAL MUSCLE; UBIQUITIN LIGASES; UP-REGULATION; WESTERN BLOTTING;

ANIMALS; MUSCLE; PELLETIZING; PHOSPHATASES;

PROTEINS;

BETA GALACTOSIDASE; GLYCOGEN; GLYCOGEN SYNTHASE; LAFORIN; MALIN; PHOSPHATASE TARGETING SUBUNIT PROTEIN TYPE 1; PROTEIN EPM2B; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; BRAIN; CELL TRANSFORMATION; CONTROLLED STUDY; ENZYME STRUCTURE; EPILEPTIC NERVE CELL; FEMALE; GENE DISRUPTION; HEART; LAFORA BODY; LIVER; MALE; MOUSE; MYOCLONUS EPILEPSY; NONHUMAN; PRIORITY JOURNAL; PROTEIN LOCALIZATION; SKELETAL MUSCLE; UPREGULATION; WESTERN BLOTTING;

ANIMALS; BLOTTING, WESTERN; BRAIN; CARRIER PROTEINS; CELLS, CULTURED; DUAL-SPECIFICITY PHOSPHATASES; HUMANS; LAFORA DISEASE; MALE; MICE; MICE, INBRED C57BL; MICE, MUTANT STRAINS; MUSCLES; POLYMERASE CHAIN REACTION; PROTEIN TYROSINE PHOSPHATASES, NON-RECEPTOR; UBIQUITIN-PROTEIN LIGASES;

ANIMALIA; MUS;

EID: 77955486949     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M110.148668     Document Type: Article

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