Cardiolipin deficiency affects respiratory chain function and organization in an induced pluripotent stem cell model of Barth syndrome

Stem Cell Research

Volumn 11, Issue 2, 2013, Pages 806-819

  Dudek, Jan ^a   Cheng, I Fen ^a,b   Balleininger, Martina ^a   Vaz, Frédéric M ^c   Streckfuss Bömeke, Katrin ^a,b   Hübscher, Daniela ^a,b   Vukotic, Milena ^a   Wanders, Ronald J A ^c   Rehling, Peter ^a,d   Guan, Kaomei ^a,b  

^a UNIVERSITY MEDICAL CENTER GÖTTINGEN   (Germany)

^b DZHK GERMAN CENTRE FOR CARDIOVASCULAR RESEARCH   (Germany)

^c UNIVERSITY OF AMSTERDAM   (Netherlands)

^d MAX PLANCK INSTITUTE FOR BIOPHYSICAL CHEMISTRY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CARDIOLIPIN; PROTEIN; REACTIVE OXYGEN METABOLITE; TAFAZZIN; UNCLASSIFIED DRUG;

ACIDIFICATION; ARTICLE; BARTH SYNDROME; BASAL METABOLIC RATE; BREATHING; CELL DIFFERENTIATION; CONTROLLED STUDY; FIBROBLAST; GERM LAYER; HUMAN; HUMAN CELL; HUMAN TISSUE; MALE; METABOLIC DISORDER; MITOCHONDRION; MUTATION; OXIDATIVE PHOSPHORYLATION; PHENOTYPE; PLURIPOTENT STEM CELL; PRIORITY JOURNAL; PROTEIN EXPRESSION; RESPIRATORY CHAIN;

ANIMALS; BARTH SYNDROME; CARDIOLIPINS; ELECTRON TRANSPORT; FIBROBLASTS; HUMANS; INDUCED PLURIPOTENT STEM CELLS; MALE; MICE;

EID: 84879493450     PISSN: 18735061     EISSN: 18767753     Source Type: Journal    
DOI: 10.1016/j.scr.2013.05.005     Document Type: Article

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