Dystrophin deficiency leads to disturbance of LAMP1-vesicle-associated protein secretion

Cellular and Molecular Life Sciences

Volumn 70, Issue 12, 2013, Pages 2159-2174

  Duguez, Stephanie ^a,b   Duddy, William ^a,b   Johnston, Helen ^a   Lainé, Jeanne ^b,c   Le Bihan, Marie Catherine ^b,c   Brown, Kristy J ^a   Bigot, Anne ^b   Hathout, Yetrib ^a   Butler Browne, Gillian ^b   Partridge, Terence ^a  

^a CHILDREN S RESEARCH INSTITUTE   (United States)

^b SORBONNE UNIVERSITÉ   (France)

^c UNIVERSITY OF SOUTHERN DENMARK   (Denmark)

Author keywords

Dystrophinopathy; LAMP; Muscle cells; SILAC; Vesicle secretion

Indexed keywords

DYSTROPHIN; LYSOSOME ASSOCIATED MEMBRANE PROTEIN 1; MYOSIN LIGHT CHAIN; MYOSIN LIGHT CHAIN 1; MYOSIN LIGHT CHAIN 3; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CYTOSOL; EXON SKIPPING; MALE; MEMBRANE VESICLE; MOUSE; MUSCLE NECROSIS; MYOTUBE; NONHUMAN; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN SECRETION;

ACTINS; AMINO ACIDS; ANIMALS; BLOTTING, WESTERN; CELL LINE; CHROMATOGRAPHY, LIQUID; COMPUTATIONAL BIOLOGY; DYSTROPHIN; IMMUNOBLOTTING; ISOTOPE LABELING; LYSOSOME-ASSOCIATED MEMBRANE GLYCOPROTEINS; MALE; MEMBRANE PROTEINS; MICE; MICROSCOPY, ELECTRON, TRANSMISSION; MUSCLE FIBERS, SKELETAL; MUSCULAR DYSTROPHY, DUCHENNE; SECRETORY VESICLES; STATISTICS, NONPARAMETRIC; TANDEM MASS SPECTROMETRY;

EID: 84878543437     PISSN: 1420682X     EISSN: 14209071     Source Type: Journal    
DOI: 10.1007/s00018-012-1248-2     Document Type: Article

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