The muscle dystrophy-causing ΔK32 lamin A/C mutant does not impair the functions of the nucleoplasmic lamin-A/C-LAP2α complex in mice

Journal of Cell Science

Volumn 126, Issue 8, 2013, Pages 1753-1762

  Pilat, Ursula ^a   Dechat, Thomas ^a   Bertrand, Anne T ^b,c   Woisetschläger, Nikola ^a   Gotic, Ivana ^a   Spilka, Rita ^a   Biadasiewicz, Katarzyna ^a   Bonne, Gisèle ^b,c,d   Foisner, Roland ^a  

^a MEDICAL UNIVERSITY OF VIENNA   (Austria)

^b Sorbonne Université   (France)

^c SORBONNE UNIVERSITÉ   (France)

^d ASSISTANCE PUBLIQUE HÔPITAUX DE PARIS   (France)

Author keywords

Congenital muscular dystrophy; Lamin A C; Lamina associated polypeptide 2 ; Nuclear envelope; Nucleoplasmic lamins

Indexed keywords

LAMIN A; LAMIN C; LAMINA ASSOCIATED POLYPEPTIDE 2ALPHA; NUCLEOPLASMIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CELL CYCLE PROGRESSION; CELL DIFFERENTIATION; CELL FUNCTION; CELLULAR DISTRIBUTION; CONTROLLED STUDY; DISEASE SEVERITY; HUMAN; MOUSE; MUSCULAR DYSTROPHY; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN PROTEIN INTERACTION; REGULATORY MECHANISM; WILD TYPE;

CONGENITAL MUSCULAR DYSTROPHY; LAMIN A/C; LAMINA ASSOCIATED POLYPEPTIDE 2Α; NUCLEAR ENVELOPE; NUCLEOPLASMIC LAMINS;

ANIMALS; CELLS, CULTURED; DNA-BINDING PROTEINS; FLUORESCENT ANTIBODY TECHNIQUE; IMMUNOHISTOCHEMISTRY; LAMIN TYPE A; MEMBRANE PROTEINS; MICE; MICE, MUTANT STRAINS; MUSCULAR DYSTROPHIES; NUCLEAR ENVELOPE; REAL-TIME POLYMERASE CHAIN REACTION;

EID: 84877951512     PISSN: 00219533     EISSN: 14779137     Source Type: Journal    
DOI: 10.1242/jcs.115246     Document Type: Article

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