Neuronatin-mediated aberrant calcium signaling and endoplasmic reticulum stress underlie neuropathology in Lafora disease

Journal of Biological Chemistry

Volumn 288, Issue 13, 2013, Pages 9482-9490

  Sharma, Jaiprakash ^a   Mukherjee, Diptendu ^a   Rao, Sudheendra N R ^a   Iyengar, Soumya ^a   Shankar, Susarla Krishna ^b   Satishchandra, Parthasarathy ^b   Jana, Nihar Ranjan ^a  

^a NATIONAL BRAIN RESEARCH CENTRE   (India)

^b NATIONAL INSTITUTE OF MENTAL HEALTH AND NEUROSCIENCES   (India)

Author keywords

[No Author keywords available]

Indexed keywords

CALCIUM SIGNALING; ECTOPIC EXPRESSIONS; ENDOPLASMIC RETICULUM STRESS; GLYCOGEN SYNTHESIS; HUMAN FETAL BRAIN; INSOLUBLE AGGREGATES; PROTEIN PHOSPHATASE; UBIQUITIN LIGASES;

BRAIN; CALCIUM; CELL DEATH; CELL MEMBRANES;

NEURONS;

CALCIUM; LAFORIN; MALIN; MEMBRANE PROTEIN; NEURONATIN; PHOSPHOPROTEIN PHOSPHATASE; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; AGE; APOPTOSIS; ARTICLE; BIOACCUMULATION; BRAIN BIOPSY; BRAIN CORTEX; CALCIUM CELL LEVEL; CALCIUM SIGNALING; CELL LOSS; CELLULAR DISTRIBUTION; CHILD; COMPLEX FORMATION; CONTROLLED STUDY; ENDOPLASMIC RETICULUM STRESS; FETUS; GABAERGIC SYSTEM; HUMAN; HUMAN CELL; HUMAN TISSUE; IN VITRO STUDY; INFANT; INTERNEURON; MYOCLONUS EPILEPSY; NERVE DEGENERATION; NEUROPATHOLOGY; PRIORITY JOURNAL; PROTEASOME DYSFUNCTION; PROTEIN AGGREGATION; PROTEIN DEFECT; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN PROTEIN INTERACTION; SCHOOL CHILD; SKIN BIOPSY; UPREGULATION;

ADOLESCENT; ADULT; AGE FACTORS; BIOPSY; BRAIN; CALCIUM; CALCIUM SIGNALING; CARRIER PROTEINS; CHILD; ENDOPLASMIC RETICULUM; HUMANS; INFANT; LAFORA DISEASE; MEMBRANE PROTEINS; MIDDLE AGED; NERVE TISSUE PROTEINS; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEIN TYROSINE PHOSPHATASES, NON-RECEPTOR; SIGNAL TRANSDUCTION; SKIN; TRANSFECTION;

EID: 84875980581     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M112.416180     Document Type: Article

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