Co-chaperone CHIP stabilizes aggregate-prone malin, a ubiquitin ligase mutated in Lafora disease

Journal of Biological Chemistry

Volumn 285, Issue 2, 2010, Pages 1404-1413

  Rao, Sudheendra N R ^a   Sharma, Jaiprakash ^a   Maity, Ranjan ^a   Jana, Nihar Ranjan ^a  

^a NATIONAL BRAIN RESEARCH CENTRE   (India)

Author keywords

[No Author keywords available]

Indexed keywords

AGGRESOMES; AUTOSOMAL RECESSIVE NEURODEGENERATIVE DISORDER; CARBOXYL TERMINUS; MISFOLDED PROTEINS; NEURONAL TISSUES; PROTEASOMES; TRANSFECTED CELLS; UBIQUITIN; UBIQUITIN LIGASES; WILD TYPES;

CELL DEATH; PROTEINS;

AGGREGATES;

CHAPERONE; HEAT SHOCK PROTEIN 70; MALIN; MUTANT PROTEIN; PROTEASOME; PROTEIN CHIP; UBIQUITIN; UBIQUITIN PROTEIN LIGASE; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG;

AGGRESOME; ANIMAL CELL; ARTICLE; CELL DEATH; CELL NUCLEUS; CONTROLLED STUDY; CYTOPLASM; EMBRYO; GENE MUTATION; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; MOUSE; MYOCLONUS EPILEPSY; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DEFECT; PROTEIN FOLDING; PROTEIN PROTEIN INTERACTION; PROTEIN STABILITY; WILD TYPE;

ANIMALS; CARRIER PROTEINS; CERCOPITHECUS AETHIOPS; COS CELLS; GLUCANS; HSC70 HEAT-SHOCK PROTEINS; HUMANS; INCLUSION BODIES; LAFORA DISEASE; MUTATION; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEIN FOLDING; PROTEIN TYROSINE PHOSPHATASES, NON-RECEPTOR; UBIQUITIN-PROTEIN LIGASES;

EID: 74049116574     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M109.006312     Document Type: Article

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