Identification of nonferritin mitochondrial iron deposits in a mouse model of Friedreich ataxia

Proceedings of the National Academy of Sciences of the United States of America

Volumn 109, Issue 50, 2012, Pages 20590-20595

  Whitnall, Megan ^a   Rahmanto, Yohan Suryo ^a   Huang, Michael L H ^a   Saletta, Federica ^a   Lok, Hiu Chuen ^a   Gutiérrez, Lucía ^b,c   Lázaro, Francisco J ^d   Fleming, Adam J ^c   St Pierre, Tim G ^c   Mikhael, Marc R ^e   Ponka, Prem ^e   Richardson, Des R ^a  

^a UNIVERSITY OF SYDNEY   (Australia)

^b INSTITUTO DE CIENCIA DE MATERIALES DE MADRID   (Spain)

^c UNIVERSITY OF WESTERN AUSTRALIA   (Australia)

^d UNIVERSITY OF ZARAGOZA   (Spain)

^e MCGILL UNIVERSITY   (Canada)

Author keywords

Ferroportin 1; Heme oxygenase; Hemojuvelin; Transferrin receptor 1

Indexed keywords

CREATINE KINASE MM; FRATAXIN; PHOSPHORUS; SULFUR; IRON; IRON BINDING PROTEIN; IRON REGULATORY PROTEIN 2;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; FRIEDREICH ATAXIA; GENE DELETION; HEART HYPERTROPHY; IRON METABOLISM; IRON STORAGE; IRON TRANSPORT; MAGNETISM; MITOCHONDRION; MOUSE; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN EXPRESSION; SIGNAL TRANSDUCTION; SIZE EXCLUSION CHROMATOGRAPHY; TRANSMISSION ELECTRON MICROSCOPY; ANIMAL; BLOOD; CARDIOMEGALY; DISEASE MODEL; DRUG ANTAGONISM; GENETICS; HEART MITOCHONDRION; HEART MUSCLE; HUMAN; IRON INTAKE; LIVER; METABOLISM; MOSSBAUER SPECTROSCOPY; MOUSE MUTANT; PATHOLOGY; ULTRASTRUCTURE;

ANIMALS; CARDIOMEGALY; CREATINE KINASE, MM FORM; DISEASE MODELS, ANIMAL; FRIEDREICH ATAXIA; HUMANS; IRON; IRON REGULATORY PROTEIN 2; IRON, DIETARY; IRON-BINDING PROTEINS; LIVER; MICE; MICE, KNOCKOUT; MICE, MUTANT STRAINS; MICROSCOPY, ELECTRON, TRANSMISSION; MITOCHONDRIA, HEART; MYOCARDIUM; SIGNAL TRANSDUCTION; SPECTROSCOPY, MOSSBAUER;

EID: 84873628363     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1215349109     Document Type: Article

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