Combination of factor H mutation and properdin deficiency causes severe C3 glomerulonephritis

Journal of the American Society of Nephrology

Volumn 24, Issue 1, 2013, Pages 53-65

  Lesher, Allison M ^a   Zhou, Lin ^a   Kimura, Yuko ^a   Sato, Sayaka ^a   Gullipalli, Damodar ^a   Herbert, Andrew P ^b   Barlow, Paul N ^b   Eberhardt, Hannes U ^c   Skerka, Christina ^c   Zipfel, Peter F ^c,d   Hamano, Takayuki ^a   Miwa, Takashi ^a   Tung, Kenneth S ^e   Song, Wen Chao ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF EDINBURGH   (United Kingdom)

^c HANS KNÖLL INSTITUTE   (Germany)

^d FRIEDRICH SCHILLER UNIVERSITY JENA   (Germany)

^e UNIVERSITY OF VIRGINIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENT FACTOR H; PROPERDIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL SURFACE; COMPLEMENT ACTIVATION; COMPLEMENT ALTERNATIVE PATHWAY; DEATH; DISEASE SEVERITY; GENE MUTATION; GLOMERULONEPHRITIS; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEFICIENCY;

EID: 84871898747     PISSN: 10466673     EISSN: 15333450     Source Type: Journal    
DOI: 10.1681/ASN.2012060570     Document Type: Article

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