Functional rescue of mutant ABCA1 proteins by sodium 4-phenylbutyrate

Journal of Lipid Research

Volumn 54, Issue 1, 2013, Pages 55-62

  Sorrenson, Brie ^a   Suetani, Rachel J ^a   Williams, Michael J A ^a   Bickley, Vivienne M ^b   George, Peter M ^b   Jones, Gregory T ^a   McCormick, Sally P A ^a  

^a UNIVERSITY OF OTAGO   (New Zealand)

^b CANTERBURY HEALTH LABORATORIES   (New Zealand)

Author keywords

Atherosclerosis; ATP binding cassette transporter; Cholesterol efflux; High density lipoprotein

Indexed keywords

4 PHENYLBUTYRIC ACID; ABC TRANSPORTER A1; HIGH DENSITY LIPOPROTEIN CHOLESTEROL; MUTANT PROTEIN;

ARTICLE; CELL MEMBRANE; CELL STRAIN HEK293; CELLULAR DISTRIBUTION; CHOLESTEROL TRANSPORT; CONTROLLED STUDY; EX VIVO STUDY; FIBROBLAST; HUMAN; HUMAN CELL; IN VITRO STUDY; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION;

ATP-BINDING CASSETTE TRANSPORTERS; CHOLESTEROL, HDL; FIBROBLASTS; HEK293 CELLS; HUMANS; MUTATION, MISSENSE; PHENYLBUTYRATES; PROTEIN TRANSPORT;

EID: 84871217016     PISSN: 00222275     EISSN: 15397262     Source Type: Journal    
DOI: 10.1194/jlr.M027193     Document Type: Article

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