Adherence issues in inherited metabolic disorders treated by low natural protein diets

Annals of Nutrition and Metabolism

Volumn 61, Issue 4, 2012, Pages 289-295

  MacDonald, A ^a   Van Rijn, M ^b   Feillet, F ^f   Lund, A M ^d   Bernstein, L ^e   Bosch, A M ^c   Gizewska, M ^g   Van Spronsen, F J ^b  

^a BIRMINGHAM CHILDREN S HOSPITAL   (United Kingdom)

^b UNIVERSITY OF GRONINGEN   (Netherlands)

^c ACADEMIC MEDICAL CENTER   (Netherlands)

^d Rigshospitalet   (Denmark)

^e CHILDREN S HOSPITAL COLORADO   (United States)

^f INSERM   (France)

^g POMERANIAN MEDICAL UNIVERSITY   (Poland)

Author keywords

Adherence; Amino acids; Dietary management; Inborn errors of metabolism; Phenylketonuria; Urea cycle disorders

Indexed keywords

AMINO ACID; ESSENTIAL AMINO ACID;

CAREGIVER SUPPORT; CLINICAL FEATURE; DISEASE SEVERITY; EARLY DIAGNOSIS; FOOD ANALYSIS; FOOD COMPOSITION; HEALTH BEHAVIOR; HOMOCYSTINURIA; HUMAN; INBORN ERROR OF METABOLISM; MAPLE SYRUP URINE DISEASE; METABOLIC REGULATION; NEUROPSYCHOLOGY; NUTRITION EDUCATION; ONSET AGE; PATIENT CARE; PATIENT COMPLIANCE; PHENYLKETONURIA; PRIORITY JOURNAL; PROTEIN RESTRICTION; REVIEW; SYMPTOM; TASTE; TREATMENT INDICATION; TYROSINEMIA;

AMINO ACIDS; DIET, PROTEIN-RESTRICTED; DIETARY SUPPLEMENTS; HUMANS; METABOLIC DISEASES; PATIENT COMPLIANCE; SOCIAL BEHAVIOR; UREA CYCLE DISORDERS, INBORN;

EID: 84870662403     PISSN: 02506807     EISSN: 14219697     Source Type: Journal    
DOI: 10.1159/000342256     Document Type: Review

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