Assessment of plasma ammonia and glutamine concentrations in urea cycle disorders

Clinical Biochemistry

Volumn 44, Issue 8-9, 2011, Pages 742-744

  Serrano, M ^a,b   Ormazabal A ^a,b   Vilaseca, M A ^a,b   Lambruschini, N ^a,b   Garcia Romero, R ^a,b   Meavilla, S ^a,b   Perez Duenas B ^a,b   Pineda, M ^a,b   Garcia Cazorla, A ^a,b   Campistol, J ^a,b   Artuch, R ^a,b  

^a HOSPITAL SANT JOAN DE DÉU   (Spain)

^b INSTITUTO DE SALUD CARLOS III   (Spain)

Author keywords

Glutamine; Hyperammonemia; Metabolic control; Pediatric patients; Urea cycle disorders

Indexed keywords

4 PHENYLBUTYRIC ACID; AMINO ACID; AMMONIA; ARGININE; CARNITINE; CITRULLINE; GLUTAMINE; PROTEIN;

ADOLESCENT; ADULT; AMMONIA BLOOD LEVEL; ARTICLE; CHILD; CLINICAL ARTICLE; CLINICAL ASSESSMENT; CONTROLLED STUDY; DISEASE ASSOCIATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FEMALE; HUMAN; INFANT; MALE; METABOLIC REGULATION; MITOCHONDRION; NEUROTOXICITY; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; UREA CYCLE DISORDER;

AMMONIA; GLUTAMINE; HUMANS; INFANT, NEWBORN; UREA CYCLE DISORDERS, INBORN;

EID: 79955841445     PISSN: 00099120     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.clinbiochem.2011.03.136     Document Type: Article

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