Nutritional management of patients with urea cycle disorders

Journal of Inherited Metabolic Disease

Volumn 30, Issue 6, 2007, Pages 880-887

  Singh, R H ^a  

^a EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALBUMIN; AMMONIA; AMMONUL; ARGINASE; ARGININE; BENZOIC ACID; BRANCHED CHAIN AMINO ACID; BUPHENYL; CITRULLINE; CLINISOL; CYCLINEX 1; DIALAMINE; ESSENTIAL AMINO ACID; GLUCOSE; INFUSION FLUID; INSULIN; ISOLEUCINE; LEUCINE; MINERAL; NITROGEN; ONDANSETRON; PARENTERAL SOLUTION; PHENYLACETATE SODIUM; PROSOL; TRAVASOL; TROPHAMINE; UNCLASSIFIED DRUG; UNINDEXED DRUG; UREA; VALINE; VAMIN 18 EF; VAMINOLACT; VITAMIN;

AMMONIA BLOOD LEVEL; CALORIC INTAKE; CITRULLINEMIA; CLINICAL FEATURE; COMA; CONGENITAL DISORDER; DIET SUPPLEMENTATION; DIETARY INTAKE; DISEASE CLASSIFICATION; DISEASE SEVERITY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; DRUG DOSE TITRATION; DRUG EFFICACY; EARLY DIAGNOSIS; EARLY INTERVENTION; ENZYME DEFICIENCY; FOOD COMPOSITION; HEMODIALYSIS; HUMAN; HYPERAMMONEMIA; LOW DRUG DOSE; MILK; NAUSEA; NEWBORN SCREENING; NOSE FEEDING; NUTRITIONAL DEFICIENCY; NUTRITIONAL REQUIREMENT; ONSET AGE; PATHOPHYSIOLOGY; POSTOPERATIVE CARE; PRACTICE GUIDELINE; PREOPERATIVE CARE; PROTEIN INTAKE; PROTEIN RESTRICTION; REVIEW; RISK ASSESSMENT; RISK FACTOR; SYMPTOM; UREA CYCLE DISORDER;

ADOLESCENT; ADULT; AMMONIA; CHILD; CHILD, PRESCHOOL; DIET THERAPY; ENZYMES; FEMALE; HUMANS; HYPERAMMONEMIA; INFANT; INFANT, NEWBORN; MALE; METABOLISM, INBORN ERRORS; MIDDLE AGED; NERVOUS SYSTEM DISEASES; NITROGEN; NUTRITIONAL SCIENCES; TREATMENT OUTCOME; UREA;

EID: 37449022958     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-007-0718-4     Document Type: Review

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