Auditory characteristics and therapeutic effects of enzyme replacement in mouse model of the mucopolysaccharidosis (MPS) II

American Journal of Medical Genetics, Part A

Volumn 158 A, Issue 9, 2012, Pages 2131-2138

  Hong, Sung Hwa ^a   Chu, Hosuk ^b   Kim, Ki Ryung ^a   Ko, Moon Hee ^a   Kwon, See Youn ^a   Moon, Il Joon ^a   Chung, Won Ho ^a   Cho, Yang Sun ^a   Kim, Chi Hwa ^c   Suh, Myung Whan ^d   Choi, Eun Wha ^c   Sohn, Young Bae ^a   Park, Sung Won ^a   Kim, Se Hwa ^a   Cho, Sung Yoon ^a   Ko, Ah Ra ^c   Jin, Dong Kyu ^a  

^a Sungkyunkwan University School of Medicine   (South Korea)

^b Hana ENT Hospital   (South Korea)

^c Samsung Medical Center   (South Korea)

^d Dankook University   (South Korea)

Author keywords

Enzyme replacement; Hearing; Hunter syndrome; Mouse model; MPS II

Indexed keywords

GLYCOSAMINOGLYCAN; IDURONATE 2 SULFATASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUDITORY THRESHOLD; COCHLEA; CONTROLLED STUDY; ENZYME REPLACEMENT; EVOKED BRAIN STEM AUDITORY RESPONSE; FEMALE; HEARING IMPAIRMENT; HISTOPATHOLOGY; HUNTER SYNDROME; INNER EAR; KNOCKOUT MOUSE; MALE; MICRO-COMPUTED TOMOGRAPHY; MIDDLE EAR EFFUSION; MOUSE; NONHUMAN; PRIORITY JOURNAL; TRANSMISSION ELECTRON MICROSCOPY; TREATMENT DURATION; WILD TYPE;

ANIMALS; AUDITORY PATHWAYS; BRAIN STEM; DISEASE MODELS, ANIMAL; EAR, MIDDLE; GLYCOSAMINOGLYCANS; IDURONATE SULFATASE; MICE; MICE, KNOCKOUT; MUCOPOLYSACCHARIDOSIS II; TOMOGRAPHY, X-RAY COMPUTED;

MUS;

EID: 84865569996     PISSN: 15524825     EISSN: 15524833     Source Type: Journal    
DOI: 10.1002/ajmg.a.35498     Document Type: Article

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