Inner ear pathology in the mucopolysaccharidosis VII mouse

Hearing Research

Volumn 169, Issue 1-2, 2002, Pages 69-84

  Ohlemiller, Kevin K ^a   Hennig, Anne K ^b   Lett, Jaclynn M ^a   Heidbreder, Arnold F ^a   Sands, Mark S ^b  

^a CENTRAL INSTITUTE FOR THE DEAF   (United States)

^b WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Glucuronidase; Cochlea; Crista; Hair cell; Lysosomal storage disease; Macula; Sly syndrome

Indexed keywords

ACID HYDROLASE; BETA GLUCURONIDASE; GLYCOSAMINOGLYCAN;

AGE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUDITORY THRESHOLD; CELL DENSITY; COCHLEA; COCHLEA FENESTRA; CONDUCTION DEAFNESS; CONTROLLED STUDY; CORTI ORGAN; EVOKED BRAIN STEM AUDITORY RESPONSE; FEMALE; HAIR CELL; HISTOPATHOLOGY; INNER EAR; INNER EAR DISEASE; LIFESPAN; LYSOSOME; LYSOSOME STORAGE DISEASE; MALE; MENTAL DEFICIENCY; MOUSE; MUCOPOLYSACCHARIDOSIS TYPE 7; NERVE CELL; NONHUMAN; PERCEPTION DEAFNESS; PRIORITY JOURNAL; SENSORY NERVE CELL; SHORT STATURE; STRIA VASCULARIS; TUNING CURVE; VESTIBULAR SYSTEM; VISUAL IMPAIRMENT; ACTION POTENTIAL; ANIMAL; CELL COUNT; DISEASE MODEL; GENETICS; HUMAN; METABOLISM; MOUSE MUTANT; PATHOLOGY; PATHOPHYSIOLOGY;

ACTION POTENTIALS; ANIMAL; AUDITORY THRESHOLD; CELL COUNT; DISEASE MODELS, ANIMAL; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; FEMALE; GLUCURONIDASE; HAIR CELLS; HEARING LOSS, CONDUCTIVE; HEARING LOSS, SENSORINEURAL; HUMAN; LABYRINTH; MALE; MICE; MICE, MUTANT STRAINS; MUCOPOLYSACCHARIDOSIS VII; SUPPORT, NON-U.S. GOV'T; SUPPORT, U.S. GOV'T, P.H.S.; ANIMALS; EAR, INNER; HUMANS;

EID: 0036019397     PISSN: 03785955     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0378-5955(02)00341-6     Document Type: Article

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