Age-related functional and histopathological changes of the ear in the MPS I mouse

International Journal of Pediatric Otorhinolaryngology

Volumn 71, Issue 2, 2007, Pages 197-203

  Schachern, Patricia A ^a   Cureoglu, Sebahattin ^a   Tsuprun, Vladimir ^a   Paparella, Michael M ^a,b   Whitley, Chester B ^a,c  

^a UNIVERSITY OF MINNESOTA   (United States)

^b Paparella Ear Head and Neck Institute PA   (United States)

^c UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

Author keywords

Auditory brainstem response; Cochlea; Ear pathology; Hearing loss; Middle ear; MPS I mouse

Indexed keywords

DERMATAN SULFATE; HEPARAN SULFATE; LEVO IDURONIDASE;

AGING; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BASILAR MEMBRANE; CONTROLLED STUDY; CORTI ORGAN; ELECTRON MICROSCOPY; ENZYME DEFICIENCY; EPITHELIUM CELL; EVOKED BRAIN STEM AUDITORY RESPONSE; GENE MUTATION; HAIR CELL; HEARING LOSS; HETEROZYGOTE; HISTOPATHOLOGY; HOMOZYGOTE; HURLER SYNDROME; INNER EAR; LYSOSOME; MESOTHELIUM CELL; MICROSCOPY; MIDDLE EAR; MOUSE; NERVE CELL; NEWBORN; NONHUMAN; PRIORITY JOURNAL; VASCULAR ENDOTHELIUM; WILD TYPE;

AGING; ANIMALS; ANIMALS, NEWBORN; DISEASE MODELS, ANIMAL; EAR; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; HEARING LOSS, SENSORINEURAL; IDURONIDASE; LYSOSOMES; MICE; MICE, KNOCKOUT; MUCOPOLYSACCHARIDOSIS I; OTITIS MEDIA;

EID: 33845987087     PISSN: 01655876     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ijporl.2006.09.016     Document Type: Article

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