Familial forms of nonspecific interstitial pneumonia/idiopathic pulmonary fibrosis: Clinical course and genetic background

Current Opinion in Pulmonary Medicine

Volumn 18, Issue 5, 2012, Pages 455-461

  Borie, Raphael ^a,b   Kannengiesser, Caroline ^a,c   Crestani, Bruno ^a,b,c  

^a BICHAT HOSPITAL   (France)

^b INSERM   (France)

^c UNIVERSITÉ PARIS DESCARTES   (France)

Author keywords

ATP binding cassette 3; MUC5B; surfactant; telomerase; telomerase reverse transcriptase

Indexed keywords

DYSKERIN; MUCIN 5B; SURFACTANT PROTEIN C; TELOMERASE; TELOMERASE REVERSE TRANSCRIPTASE;

ABNORMAL RESPIRATORY SOUND; ACUTE LEUKEMIA; ANEMIA; APLASTIC ANEMIA; COMPUTER ASSISTED TOMOGRAPHY; CPG ISLAND; DISEASE COURSE; DNA POLYMORPHISM; DNA SEQUENCE; DYSKERATOSIS CONGENITA; DYSPNEA; EPIGENETICS; FAMILIAL INTERSTITIAL PNEUMONIA; FIBROSING ALVEOLITIS; GENE CONTROL; GENE MUTATION; GENETIC ASSOCIATION; HEREDITY; HETEROZYGOTE; HUMAN; INTERSTITIAL PNEUMONIA; LEUKOCYTE; LUNG BIOPSY; LUNG FUNCTION; LYMPHADENOPATHY; MYELODYSPLASTIC SYNDROME; PROMOTER REGION; PROTEIN EXPRESSION; REVIEW; SIGNAL TRANSDUCTION; VERTICAL TRANSMISSION;

FEMALE; HUMANS; IDIOPATHIC PULMONARY FIBROSIS; LUNG DISEASES, INTERSTITIAL; MALE; MUCIN-5B; MUTATION; PEDIGREE; PULMONARY SURFACTANT-ASSOCIATED PROTEIN C; RNA; TELOMERASE;

EID: 84864869869     PISSN: 10705287     EISSN: 15316971     Source Type: Journal    
DOI: 10.1097/MCP.0b013e328356b15c     Document Type: Review

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