Usual interstitial pneumonia in an adolescent with ABCA3 mutations

Chest

Volumn 134, Issue 1, 2008, Pages 192-195

  Young, Lisa R ^a   Nogee, Lawrence M ^c   Barnett, Bruce ^d   Panos, Ralph J ^b   Colby, Thomas V ^e   Deutsch, Gail H ^a  

^a CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^b UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

^c JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d Toledo Children's Hospital   (United States)

^e MAYO CLINIC   (United States)

Author keywords

ABCA3; Children; Interstitial lung disease; Surfactant; Usual interstitial pneumonia

Indexed keywords

ADENOSINE TRIPHOSPHATE BINDING CASSETTE A3; CARRIER PROTEINS AND BINDING PROTEINS; LUNG SURFACTANT;

ADOLESCENT; ANAMNESIS; ARTICLE; BRONCHOSCOPY; CASE REPORT; CLINICAL FEATURE; CODON; EXON; FORCED EXPIRATORY VOLUME; GENE MUTATION; GENETIC ANALYSIS; HIGH RESOLUTION COMPUTER TOMOGRAPHY; HUMAN; HUMAN TISSUE; INTERSTITIAL PNEUMONIA; INTRON; LABORATORY TEST; LUNG BIOPSY; LUNG FIBROSIS; LUNG FUNCTION TEST; MALE; PHYSICAL EXAMINATION; PRIORITY JOURNAL; RNA SPLICING; THORACOSCOPY;

EID: 47549116428     PISSN: 00123692     EISSN: None     Source Type: Journal    
DOI: 10.1378/chest.07-2652     Document Type: Article

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