HHV-8-related hemophagocytic lymphohistiocytosis in a boy with XLP phenotype

Journal of Pediatric Hematology/Oncology

Volumn 34, Issue 6, 2012, Pages 467-471

  Pasic, Srdjan ^a   Cupic, Maja ^b   Lazarevic, Ivana ^b  

^a UNIVERSITY OF BELGRADE   (Serbia)

^b UNIVERSITY OF BELGRADE   (Serbia)

Author keywords

hemophagocytic ymphohistiocytosis; human herpesvirus 8; X linked lymphoproliferative disease

Indexed keywords

ANTIBIOTIC AGENT; CYCLOSPORIN; DEXAMETHASONE; EPIRUBICIN; FERRITIN; IMMUNOGLOBULIN; LACTATE DEHYDROGENASE; PREDNISONE; TRIACYLGLYCEROL;

ARTICLE; CASE REPORT; CEREBROSPINAL FLUID EXAMINATION; CHILD; COMPUTER ASSISTED TOMOGRAPHY; CONTROLLED STUDY; DIFFERENTIAL DIAGNOSIS; DISEASE ASSOCIATION; DISEASE PREDISPOSITION; DRUG TREATMENT FAILURE; EPSTEIN BARR VIRUS; EYELID EDEMA; FERRITIN BLOOD LEVEL; FEVER; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HEPATOSPLENOMEGALY; HUMAN; HUMAN HERPESVIRUS 8; HUMAN TISSUE; IMMUNOTHERAPY; JOINT SWELLING; JUVENILE RHEUMATOID ARTHRITIS; LACTATE DEHYDROGENASE BLOOD LEVEL; LIMB PAIN; MACULOPAPULAR RASH; MALE; MUCOCUTANEOUS LYMPH NODE SYNDROME; NIGHT SWEAT; OUTCOME ASSESSMENT; PHENOTYPE; PLEOCYTOSIS; PRESCHOOL CHILD; PRIORITY JOURNAL; RARE DISEASE; TRIACYLGLYCEROL BLOOD LEVEL; X CHROMOSOME LINKED DISORDER;

CHILD, PRESCHOOL; HERPESVIRIDAE INFECTIONS; HERPESVIRUS 8, HUMAN; HUMANS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; LYMPHOPROLIFERATIVE DISORDERS; MALE; PHENOTYPE; PROGNOSIS;

EID: 84864373662     PISSN: 10774114     EISSN: 15363678     Source Type: Journal    
DOI: 10.1097/MPH.0b013e3182375372     Document Type: Article

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