Lymphocytic vasculitis involving the central nervous system occurs in patients with X-linked lymphoproliferative disease in the absence of Epstein-Barr virus infection

Pediatric Blood and Cancer

Volumn 53, Issue 6, 2009, Pages 1120-1123

  Talaat, Kawsar R ^a,d   Rothman, Jennifer A ^b   Cohen, Jeffrey I ^a   Santi, Mariarita ^b   Choi, John K ^b   Guzman, Miguel ^b   Zimmerman, Robert ^b   Nallasamy, Sudha ^c   Brucker, Alexander ^c   Quezado, Martha ^a   Pittaluga, Stefania ^a   Patronas, Nicholas J ^a   Klion, Amy D ^a   Nichols, Kim E ^b  

^a NATIONAL INSTITUTES OF HEALTH   (United States)

^b CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^c PENN PRESBYTERIAN MEDICAL CENTER   (United States)

^d JOHNS HOPKINS BLOOMBERG SCHOOL OF PUBLIC HEALTH   (United States)

Author keywords

Central nervous system; Vasculitis; X linked lymphoproliferative disease

Indexed keywords

ALEMTUZUMAB; ARGININE; CYCLOPHOSPHAMIDE; DEXAMETHASONE; ETOPOSIDE; IMMUNOGLOBULIN; IMMUNOGLOBULIN A; IMMUNOGLOBULIN M; METHOTREXATE; METHYLPREDNISOLONE; RAPAMYCIN; RITUXIMAB; SIGNALING LYMPHOCYTE ACTIVATION MOLECULE ASSOCIATED PROTEIN;

ADULT; ANEMIA; ARTICLE; BLURRED VISION; BRAIN VASCULITIS; CASE REPORT; EPSTEIN BARR VIRUS; FEVER; HEADACHE; HUMAN; IMMUNE RESPONSE; IMMUNOGLOBULIN BLOOD LEVEL; JAUNDICE; LYMPHOCYTIC VASCULITIS; LYMPHOMA; LYMPHOPROLIFERATIVE DISEASE; MALE; MUTATIONAL ANALYSIS; PRIORITY JOURNAL; PROTEIN FUNCTION; SEROLOGY; STOP CODON; T LYMPHOCYTE; T LYMPHOCYTE ACTIVATION; UPPER RESPIRATORY TRACT INFECTION; VASCULITIS; VIRUS INFECTION; X LINKED LYMPHOPROLIFERATIVE DISEASE;

ADOLESCENT; ADULT; CENTRAL NERVOUS SYSTEM; EPSTEIN-BARR VIRUS INFECTIONS; FATAL OUTCOME; GENETIC DISEASES, X-LINKED; HUMANS; INTRACELLULAR SIGNALING PEPTIDES AND PROTEINS; LYMPHATIC VESSELS; LYMPHOPROLIFERATIVE DISORDERS; MALE; T-LYMPHOCYTES; VASCULITIS;

EID: 71049158087     PISSN: 15455009     EISSN: 15455017     Source Type: Journal    
DOI: 10.1002/pbc.22185     Document Type: Article

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