Differential response to intracellular stress in the skin from osteogenesis imperfecta Brtl mice with lethal and non lethal phenotype: A proteomic approach

Journal of Proteomics

Volumn 75, Issue 15, 2012, Pages 4717-4733

  Bianchi, Laura ^a   Gagliardi, Assunta ^a   Gioia, Roberta ^b   Besio, Roberta ^b   Tani, Chiara ^c   Landi, Claudia ^a   Cipriano, Maria ^a   Gimigliano, Anna ^a   Rossi, Antonio ^b   Marini, Joan C ^d   Forlino, Antonella ^b   Bini, Luca ^a  

^a UNIVERSITY OF SIENA   (Italy)

^b UNIVERSITY OF PAVIA   (Italy)

^c NOVARTIS VACCINES AND DIAGNOSTICS   (Italy)

^d EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

Chaperones; Functional proteomics; Hierarchical clustering; Osteogenesis imperfecta; Pathway analysis; Proteasomal

Indexed keywords

ALPHA CRYSTALLIN; ALPHA ENOLASE; BETA ACTIN; CALRETICULIN; COFILIN 1; COLLAGEN TYPE 1; GALECTIN 7; KERATIN; MASPIN; OCTAMER TRANSCRIPTION FACTOR 4; VIMENTIN;

AMINO ACID SUBSTITUTION; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL FATE; CELLULAR STRESS RESPONSE; CONTROLLED STUDY; CYTOSKELETON; FUNCTIONAL PROTEOMICS; GENETIC VARIABILITY; MOUSE; NONHUMAN; OSTEOGENESIS IMPERFECTA; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FOLDING; SKIN;

AMINO ACID SUBSTITUTION; ANIMALS; COLLAGEN TYPE I; DISEASE MODELS, ANIMAL; HUMANS; MICE; MICE, MUTANT STRAINS; MUTATION, MISSENSE; OSTEOGENESIS IMPERFECTA; PHENOTYPE; PROTEOME; PROTEOMICS; SKIN; STRESS, PHYSIOLOGICAL;

ANIMALIA; MURINAE; MUS;

EID: 84864103824     PISSN: 18743919     EISSN: 18767737     Source Type: Journal    
DOI: 10.1016/j.jprot.2012.01.038     Document Type: Article

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