Use of the Cre/lox recombination system to develop a non-lethal knock-in murine model for osteogenesis imperfecta with an α1(I) G349C substitution. Variability in phenotype in BrtlIV mice

Journal of Biological Chemistry

Volumn 274, Issue 53, 1999, Pages 37923-37931

  Forlino, Antonella ^a   Porter, Forbes D ^a   Eric J, Lee ^a   Westphal, Heiner ^a   Marini, Joan C ^a  

^a EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

RIBOZYME;

ALLELE; AMINO ACID SUBSTITUTION; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHIMERA; CONTROLLED STUDY; EXPERIMENTAL ANIMAL; FEMALE; GENE CASSETTE; GENE EXPRESSION; GENE MUTATION; GENETIC RECOMBINATION; GENETIC VARIABILITY; GENOTYPE; KNOCKOUT MOUSE; MALE; MOUSE; NONHUMAN; OSTEOGENESIS IMPERFECTA; PHENOTYPE; PRIORITY JOURNAL;

ALTERNATIVE SPLICING; AMINO ACID SUBSTITUTION; ANIMALS; BASE SEQUENCE; CHIMERA; COLLAGEN; CYSTEINE; DISEASE MODELS, ANIMAL; FEMALE; GLYCINE; HETEROZYGOTE; HUMANS; INTEGRASES; MALE; MICE; MICE, MUTANT STRAINS; MOLECULAR SEQUENCE DATA; OSTEOGENESIS IMPERFECTA; PHENOTYPE; RNA, MESSENGER; VIRAL PROTEINS;

ANIMALIA; MURINAE; RODENTIA;

EID: 0033621331     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.274.53.37923     Document Type: Article

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