Expression of Fraser syndrome genes in normal and polycystic murine kidneys

Pediatric Nephrology

Volumn 27, Issue 6, 2012, Pages 991-998

  Kerecuk, Larissa ^a,b   Long, David A ^a   Ali, Zahabia ^a   Anders, Corina ^c   Kolatsi Joannou, Maria ^a   Scambler, Peter J ^a   Woolf, Adrian S ^c  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b BIRMINGHAM CHILDREN S HOSPITAL   (United Kingdom)

^c UNIVERSITY OF MANCHESTER   (United Kingdom)

Author keywords

Basement membrane; Cyst; Development; Fras1 . Frem2; LacZ; Reporter gene

Indexed keywords

AQUAPORIN 2; BETA GALACTOSIDASE; DEXAMETHASONE; FRASI RELATED EXTRACELLULAR MATRIX PROTEIN 2; PROTEIN; TAMM HORSFALL GLYCOPROTEIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; DOWN REGULATION; FRASER SYNDROME; GENE EXPRESSION; GENE LOCUS; GLOMERULUS; HAPLOINSUFFICIENCY; HENLE LOOP; HETEROZYGOTE; HISTOLOGY; HOMOZYGOSITY; IMMUNOHISTOCHEMISTRY; IN VIVO STUDY; KIDNEY CORTEX; KIDNEY FAILURE; KIDNEY HYPERTROPHY; KIDNEY MASS; KIDNEY MEDULLA; KIDNEY POLYCYSTIC DISEASE; KIDNEY PROXIMAL TUBULE; KIDNEY TUBULE EPITHELIUM; MOUSE; NEPHRON; NONHUMAN; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN EXPRESSION; PROTEIN FUNCTION; RAT; UREMIA;

ANIMALS; DEXAMETHASONE; DISEASE MODELS, ANIMAL; EMBRYO CULTURE TECHNIQUES; EXTRACELLULAR MATRIX PROTEINS; FRASER SYNDROME; GENE EXPRESSION REGULATION; GENES, REPORTER; IMMUNOHISTOCHEMISTRY; LAC OPERON; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MUTATION; NEPHRONS; POLYCYSTIC KIDNEY, AUTOSOMAL RECESSIVE; RATS; RECEPTORS, CELL SURFACE;

EID: 84863989575     PISSN: 0931041X     EISSN: 1432198X     Source Type: Journal    
DOI: 10.1007/s00467-012-2100-5     Document Type: Article

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