Cytochrome c oxidase-intermediate fibres: Importance in understanding the pathogenesis and treatment of mitochondrial myopathy

Neuromuscular Disorders

Volumn 22, Issue 8, 2012, Pages 690-698

  Murphy, Julie L ^a   Ratnaike, Thiloka E ^a   Shang, Ersong ^a   Falkous, Gavin ^a   Blakely, Emma L ^a   Alston, Charlotte L ^a   Taivassalo, Tanja ^b   Haller, Ronald G ^c,d   Taylor, Robert W ^a   Turnbull, Doug M ^a  

^a NEWCASTLE UNIVERSITY   (United Kingdom)

^b MCGILL UNIVERSITY   (Canada)

^c Environmental Medicine of Texas Health Presbyterian Hospital   (United States)

^d UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

Cytochrome c oxidase; Enzyme histochemistry; Mitochondrial myopathy; MtDNA

Indexed keywords

CYTOCHROME C OXIDASE; MITOCHONDRIAL DNA; SUCCINATE DEHYDROGENASE;

ARTICLE; CELL POPULATION; CLINICAL ARTICLE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME DEFICIENCY; ENZYME MECHANISM; GENE MUTATION; HISTOCHEMISTRY; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOCYTOCHEMISTRY; MITOCHONDRIAL MYOPATHY; MUSCLE BIOPSY; MUSCLE CELL; PATHOGENESIS; PRIORITY JOURNAL; RESPIRATORY CHAIN; WILD TYPE;

BIOPSY; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT COMPLEX IV; HISTOCYTOCHEMISTRY; HUMANS; MITOCHONDRIAL MYOPATHIES; MUSCLE FIBERS, SKELETAL; MUSCLE, SKELETAL; MUTATION; SUCCINATE DEHYDROGENASE;

EID: 84863874248     PISSN: 09608966     EISSN: 18732364     Source Type: Journal    
DOI: 10.1016/j.nmd.2012.04.003     Document Type: Article

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