Haploinsufficiency of utrophin gene worsens skeletal muscle inflammation and fibrosis in mdx mice

Journal of the Neurological Sciences

Volumn 264, Issue 1-2, 2008, Pages 106-111

  Zhou, Lan ^a   Rafael Fortney, Jill A ^b   Huang, Ping ^a   Zhao, Xinyu S ^a   Cheng, Georgiana ^c   Zhou, Xiaohua ^c   Kaminski, Henry J ^c   Liu, Liping ^a   Ransohoff, Richard M ^a  

^a LERNER RESEARCH INSTITUTE   (United States)

^b OHIO STATE UNIVERSITY   (United States)

^c CASE WESTERN RESERVE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Duchenne muscular dystrophy; Fibrosis; Inflammation; Mdx; Mdx utrn+ ; Mouse model

Indexed keywords

DYSTROPHIN; UTROPHIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DIAPHRAGM; DIAPHRAGM MUSCLE; DUCHENNE MUSCULAR DYSTROPHY; FIBROSIS; GENE; LIFESPAN; MALE; MOUSE; MUSCULAR DYSTROPHY; MYOSITIS; NONHUMAN; PRIORITY JOURNAL; QUADRICEPS FEMORIS MUSCLE; QUALITATIVE ANALYSIS; QUANTITATIVE ANALYSIS; UTROPHIN GENE; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE;

AGE FACTORS; AGING; ANIMALS; DIAPHRAGM; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; DYSTROPHIN; FIBROSIS; GENETIC PREDISPOSITION TO DISEASE; HAPLOTYPES; LONGEVITY; MALE; MICE; MICE, INBRED MDX; MICE, KNOCKOUT; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, DUCHENNE; MUTATION; MYOSITIS; QUADRICEPS MUSCLE; UTROPHIN;

EID: 36549027365     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jns.2007.08.029     Document Type: Article

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