-
1
-
-
0023614188
-
Dystrophin: the protein product of the Duchenne muscular dystrophy locus
-
Hoffman E.P., Brown R.H., Kunkel L.M. Dystrophin: the protein product of the Duchenne muscular dystrophy locus. Cell 1987, 51:919-928.
-
(1987)
Cell
, vol.51
, pp. 919-928
-
-
Hoffman, E.P.1
Brown, R.H.2
Kunkel, L.M.3
-
2
-
-
0036087342
-
Function and genetics of dystrophin and dystrophin-related proteins in muscle
-
Blake D.J., Weir A., Newey S.E., Davies K.E. Function and genetics of dystrophin and dystrophin-related proteins in muscle. Physiol Rev 2002, 82:291-329.
-
(2002)
Physiol Rev
, vol.82
, pp. 291-329
-
-
Blake, D.J.1
Weir, A.2
Newey, S.E.3
Davies, K.E.4
-
3
-
-
0034638834
-
Expression profiling in the muscular dystrophies: identification of novel aspects of molecular pathophysiology
-
Chen Y.W., Zhao P., Borup R., Hoffman E.P. Expression profiling in the muscular dystrophies: identification of novel aspects of molecular pathophysiology. J Cell Biol 2000, 151:1321-1336.
-
(2000)
J Cell Biol
, vol.151
, pp. 1321-1336
-
-
Chen, Y.W.1
Zhao, P.2
Borup, R.3
Hoffman, E.P.4
-
4
-
-
33745168598
-
Muscle damage in mdx (dystrophic) mice: role of calcium and reactive oxygen species
-
Whitehead N.P., Yeung E.W., Allen D.G. Muscle damage in mdx (dystrophic) mice: role of calcium and reactive oxygen species. Clin Exp Pharmacol Physiol 2006, 33:657-662.
-
(2006)
Clin Exp Pharmacol Physiol
, vol.33
, pp. 657-662
-
-
Whitehead, N.P.1
Yeung, E.W.2
Allen, D.G.3
-
5
-
-
33947258069
-
Pathophysiology of Duchenne muscular dystrophy: current hypotheses
-
Deconinck N., Dan B. Pathophysiology of Duchenne muscular dystrophy: current hypotheses. Pediatr Neurol 2007, 36:1-7.
-
(2007)
Pediatr Neurol
, vol.36
, pp. 1-7
-
-
Deconinck, N.1
Dan, B.2
-
6
-
-
0024353559
-
The molecular basis of muscular dystrophy in the mdx mouse: a point mutation
-
Sicinski P., Geng Y., Ryder-Cook A.S., Barnard E.A., Darlison M.G., Barnard P.J. The molecular basis of muscular dystrophy in the mdx mouse: a point mutation. Science 1989, 244:1578-1580.
-
(1989)
Science
, vol.244
, pp. 1578-1580
-
-
Sicinski, P.1
Geng, Y.2
Ryder-Cook, A.S.3
Barnard, E.A.4
Darlison, M.G.5
Barnard, P.J.6
-
7
-
-
45049087094
-
Towards developing standard operating procedures for pre-clinical testing in the mdx mouse model of Duchenne muscular dystrophy
-
Grounds M.D., Radley H.G., Lynch G.S., Nagaraju K., De Luca A. Towards developing standard operating procedures for pre-clinical testing in the mdx mouse model of Duchenne muscular dystrophy. Neurobiol Dis 2008, 31:1-19.
-
(2008)
Neurobiol Dis
, vol.31
, pp. 1-19
-
-
Grounds, M.D.1
Radley, H.G.2
Lynch, G.S.3
Nagaraju, K.4
De Luca, A.5
-
8
-
-
34347374860
-
Dystrophin-deficient mdx mice display a reduced life span and are susceptible to spontaneous rhabdomyosarcoma
-
Chamberlain J.S., Metzger J., Reyes M., Townsend D., Faulkner J.A. Dystrophin-deficient mdx mice display a reduced life span and are susceptible to spontaneous rhabdomyosarcoma. FASEB J 2007, 21:2195-2204.
-
(2007)
FASEB J
, vol.21
, pp. 2195-2204
-
-
Chamberlain, J.S.1
Metzger, J.2
Reyes, M.3
Townsend, D.4
Faulkner, J.A.5
-
9
-
-
0036823499
-
The role of utrophin in the potential therapy of Duchenne muscular dystrophy
-
Perkins K.J., Davies K.E. The role of utrophin in the potential therapy of Duchenne muscular dystrophy. Neuromuscul Disord 2002, 12(Suppl. 1):S78-S89.
-
(2002)
Neuromuscul Disord
, vol.12
, Issue.1 SUPPL.
-
-
Perkins, K.J.1
Davies, K.E.2
-
10
-
-
53749088724
-
Gentamicin treatment in exercised mdx mice: identification of dystrophin-sensitive pathways and evaluation of efficacy in work-loaded dystrophic muscle
-
De Luca A., Nico B., Rolland J.F., Cozzoli A., Burdi R., Mangieri D., et al. Gentamicin treatment in exercised mdx mice: identification of dystrophin-sensitive pathways and evaluation of efficacy in work-loaded dystrophic muscle. Neurobiol Dis 2008, 32:243-253.
-
(2008)
Neurobiol Dis
, vol.32
, pp. 243-253
-
-
De Luca, A.1
Nico, B.2
Rolland, J.F.3
Cozzoli, A.4
Burdi, R.5
Mangieri, D.6
-
11
-
-
43449105011
-
Dystrophin-deficient cardiomyopathy in mouse: expression of Nox4 and Lox are associated with fibrosis and altered functional parameters in the heart
-
Spurney C.F., Knoblach S., Pistilli E.E., Nagaraju K., Martin G.R., Hoffman E.P. Dystrophin-deficient cardiomyopathy in mouse: expression of Nox4 and Lox are associated with fibrosis and altered functional parameters in the heart. Neuromuscul Disord 2008, 18:371-381.
-
(2008)
Neuromuscul Disord
, vol.18
, pp. 371-381
-
-
Spurney, C.F.1
Knoblach, S.2
Pistilli, E.E.3
Nagaraju, K.4
Martin, G.R.5
Hoffman, E.P.6
-
12
-
-
33646032109
-
Gene expression profiling to monitor therapeutic and adverse effects of antisense therapies for Duchenne muscular dystrophy
-
't Hoen P.A., van der Wees C.G., Aartsma-Rus A., Turk R., Goyenvalle A., Danos O., et al. Gene expression profiling to monitor therapeutic and adverse effects of antisense therapies for Duchenne muscular dystrophy. Pharmacogenomics 2006, 7:281-297.
-
(2006)
Pharmacogenomics
, vol.7
, pp. 281-297
-
-
't Hoen, P.A.1
van der Wees, C.G.2
Aartsma-Rus, A.3
Turk, R.4
Goyenvalle, A.5
Danos, O.6
-
13
-
-
0027984229
-
Voluntary exercise decreases progression of muscular dystrophy in diaphragm of mdx mice
-
Dupont-Versteegden E.E., McCarter R.J., Katz M.S. Voluntary exercise decreases progression of muscular dystrophy in diaphragm of mdx mice. J Appl Physiol 1994, 77:1736-1741.
-
(1994)
J Appl Physiol
, vol.77
, pp. 1736-1741
-
-
Dupont-Versteegden, E.E.1
McCarter, R.J.2
Katz, M.S.3
-
14
-
-
41549141793
-
Reduced muscle necrosis and long-term benefits in dystrophic mdx mice after cV1q (blockade of TNF) treatment
-
Radley H.G., Davies M.J., Grounds M.D. Reduced muscle necrosis and long-term benefits in dystrophic mdx mice after cV1q (blockade of TNF) treatment. Neuromuscul Disord 2008, 18:227-238.
-
(2008)
Neuromuscul Disord
, vol.18
, pp. 227-238
-
-
Radley, H.G.1
Davies, M.J.2
Grounds, M.D.3
-
15
-
-
0037347757
-
Comparison of quantification of histochemical staining by hue-saturation-intensity (HSI) transformation and color-deconvolution
-
Ruifrok A.C., Katz R.L., Johnston D.A. Comparison of quantification of histochemical staining by hue-saturation-intensity (HSI) transformation and color-deconvolution. Appl Immunohistochem Mol Morphol 2003, 11:85-91.
-
(2003)
Appl Immunohistochem Mol Morphol
, vol.11
, pp. 85-91
-
-
Ruifrok, A.C.1
Katz, R.L.2
Johnston, D.A.3
-
16
-
-
0034810216
-
Three mouse models of muscular dystrophy: the natural history of strength and fatigue in dystrophin-, dystrophin/utrophin-, and laminin alpha2-deficient mice
-
Connolly A.M., Keeling R.M., Mehta S., Pestronk A., Sanes J.R. Three mouse models of muscular dystrophy: the natural history of strength and fatigue in dystrophin-, dystrophin/utrophin-, and laminin alpha2-deficient mice. Neuromuscul Disord 2001, 11:703-712.
-
(2001)
Neuromuscul Disord
, vol.11
, pp. 703-712
-
-
Connolly, A.M.1
Keeling, R.M.2
Mehta, S.3
Pestronk, A.4
Sanes, J.R.5
-
17
-
-
53049100736
-
Prevention of muscle fibrosis and improvement in muscle performance in the mdx mouse by halofuginone
-
Turgeman T., Hagai Y., Huebner K., Jassal D.S., Anderson J.E., Genin O., et al. Prevention of muscle fibrosis and improvement in muscle performance in the mdx mouse by halofuginone. Neuromuscul Disord 2008, 18:857-868.
-
(2008)
Neuromuscul Disord
, vol.18
, pp. 857-868
-
-
Turgeman, T.1
Hagai, Y.2
Huebner, K.3
Jassal, D.S.4
Anderson, J.E.5
Genin, O.6
-
18
-
-
0036903174
-
Adaptations of skeletal muscle to exercise: rapid increase in the transcriptional coactivator PGC-1
-
Baar K., Wende A.R., Jones T.E., Marison M., Nolte L.A., Chen M., et al. Adaptations of skeletal muscle to exercise: rapid increase in the transcriptional coactivator PGC-1. FASEB J 2002, 16:1879-1886.
-
(2002)
FASEB J
, vol.16
, pp. 1879-1886
-
-
Baar, K.1
Wende, A.R.2
Jones, T.E.3
Marison, M.4
Nolte, L.A.5
Chen, M.6
-
19
-
-
65949114863
-
Preclinical drug trials in the mdx mouse: assessment of reliable and sensitive outcome measures
-
Spurney C.F., Gordish-Dressman H., Guerron A.D., Sali A., Pandey G.S., Rawat R., et al. Preclinical drug trials in the mdx mouse: assessment of reliable and sensitive outcome measures. Muscle Nerve 2009, 39:591-602.
-
(2009)
Muscle Nerve
, vol.39
, pp. 591-602
-
-
Spurney, C.F.1
Gordish-Dressman, H.2
Guerron, A.D.3
Sali, A.4
Pandey, G.S.5
Rawat, R.6
-
20
-
-
63749096532
-
Mammalian animal models for Duchenne muscular dystrophy
-
Willmann R., Possekel S., Dubach-Powell J., Meier T., Ruegg M.A. Mammalian animal models for Duchenne muscular dystrophy. Neuromuscul Disord 2009, 19:241-249.
-
(2009)
Neuromuscul Disord
, vol.19
, pp. 241-249
-
-
Willmann, R.1
Possekel, S.2
Dubach-Powell, J.3
Meier, T.4
Ruegg, M.A.5
-
21
-
-
0031980295
-
Contractile function and low-intensity exercise effects of old dystrophic (mdx) mice
-
Hayes A., Williams D.A. Contractile function and low-intensity exercise effects of old dystrophic (mdx) mice. Am J Physiol 1998, 274:C1138-C1144.
-
(1998)
Am J Physiol
, vol.274
-
-
Hayes, A.1
Williams, D.A.2
-
22
-
-
0029000370
-
Effect of voluntary wheel-running exercise on muscles of the mdx mouse
-
Carter G.T., Wineinger M.A., Walsh S.A., Horasek S.J., Abresch R.T., Fowler W.M. Effect of voluntary wheel-running exercise on muscles of the mdx mouse. Neuromuscul Disord 1995, 5:323-332.
-
(1995)
Neuromuscul Disord
, vol.5
, pp. 323-332
-
-
Carter, G.T.1
Wineinger, M.A.2
Walsh, S.A.3
Horasek, S.J.4
Abresch, R.T.5
Fowler, W.M.6
-
23
-
-
0037215644
-
Enhanced dystrophic progression in mdx mice by exercise and beneficial effects of taurine and insulin-like growth factor-1
-
De Luca A., Pierno S., Liantonio A., Cetrone M., Camerino C., Fraysse B., et al. Enhanced dystrophic progression in mdx mice by exercise and beneficial effects of taurine and insulin-like growth factor-1. J Pharmacol Exp Ther 2003, 304:453-463.
-
(2003)
J Pharmacol Exp Ther
, vol.304
, pp. 453-463
-
-
De Luca, A.1
Pierno, S.2
Liantonio, A.3
Cetrone, M.4
Camerino, C.5
Fraysse, B.6
-
25
-
-
17744370728
-
Decreased mitochondrial oxygen consumption and antioxidant enzyme activities in skeletal muscle of dystrophic mice after low-intensity exercise
-
Faist V., Konig J., Hoger H., Elmadfa I. Decreased mitochondrial oxygen consumption and antioxidant enzyme activities in skeletal muscle of dystrophic mice after low-intensity exercise. Ann Nutr Metab 2001, 45:58-66.
-
(2001)
Ann Nutr Metab
, vol.45
, pp. 58-66
-
-
Faist, V.1
Konig, J.2
Hoger, H.3
Elmadfa, I.4
-
26
-
-
0031924679
-
Evidence of mdx mouse skeletal muscle fragility in vivo by eccentric running exercise
-
Vilquin J.T., Brussee V., Asselin I., Kinoshita I., Gingras M., Tremblay J.P. Evidence of mdx mouse skeletal muscle fragility in vivo by eccentric running exercise. Muscle Nerve 1998, 21:567-576.
-
(1998)
Muscle Nerve
, vol.21
, pp. 567-576
-
-
Vilquin, J.T.1
Brussee, V.2
Asselin, I.3
Kinoshita, I.4
Gingras, M.5
Tremblay, J.P.6
-
27
-
-
34247647576
-
Strength and corticosteroid responsiveness of mdx mice is unchanged by RAG2 gene knockout
-
Golumbek P.T., Keeling R.M., Connolly A.M. Strength and corticosteroid responsiveness of mdx mice is unchanged by RAG2 gene knockout. Neuromuscul Disord 2007, 17:376-384.
-
(2007)
Neuromuscul Disord
, vol.17
, pp. 376-384
-
-
Golumbek, P.T.1
Keeling, R.M.2
Connolly, A.M.3
-
28
-
-
42649127369
-
Mdx respiratory impairment following fibrosis of the diaphragm
-
Ishizaki M., Suga T., Kimura E., Shiota T., Kawano R., Uchida Y., et al. Mdx respiratory impairment following fibrosis of the diaphragm. Neuromuscul Disord 2008, 18:342-348.
-
(2008)
Neuromuscul Disord
, vol.18
, pp. 342-348
-
-
Ishizaki, M.1
Suga, T.2
Kimura, E.3
Shiota, T.4
Kawano, R.5
Uchida, Y.6
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