Development of IgA nephropathy-like glomerulonephritis associated with Wiskott-Aldrich syndrome protein deficiency

Clinical Immunology

Volumn 142, Issue 2, 2012, Pages 160-166

  Shimizu, M ^a,b   Nikolov, N P ^c,d   Ueno, K ^b   Ohta, K ^b,e   Siegel, R M ^c   Yachie, A ^b   Candotti, F ^a  

^a NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

^b KANAZAWA UNIVERSITY   (Japan)

^c NATIONAL INSTITUTE OF ARTHRITIS AND MUSCULOSKELETAL AND SKIN DISEASES   (United States)

^d CENTER FOR DRUG EVALUATION AND RESEARCH   (United States)

^e NATIONAL HOSPITAL ORGANIZATION KANAZAWA MEDICAL CENTER   (Japan)

Author keywords

Glycosylation; IgA; IgA nephropathy; Wiskott Aldrich syndrome

Indexed keywords

IMMUNOGLOBULIN A ANTIBODY; WISKOTT ALDRICH SYNDROME PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANTIBODY PRODUCING CELL; ARTICLE; B LYMPHOCYTE; BLOOD SAMPLING; CONTROLLED STUDY; ENZYME LINKED IMMUNOSORBENT ASSAY; HISTOPATHOLOGY; IMMUNE COMPLEX DEPOSITION; IMMUNOGLOBULIN A NEPHROPATHY; IMMUNOGLOBULIN BLOOD LEVEL; IN VITRO STUDY; IN VIVO STUDY; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROLIFERATIVE GLOMERULONEPHRITIS; PROTEIN GLYCOSYLATION; SPLEEN; SPLEEN CELL; WILD TYPE; WISKOTT ALDRICH SYNDROME;

ANIMALS; B-LYMPHOCYTES; DISEASE MODELS, ANIMAL; GLOMERULONEPHRITIS, IGA; GLYCOSYLATION; HUMANS; IMMUNOGLOBULIN A; MICE; MICE, KNOCKOUT; SPLEEN; THROMBOCYTOPENIA; WISKOTT-ALDRICH SYNDROME; WISKOTT-ALDRICH SYNDROME PROTEIN;

EID: 84856527556     PISSN: 15216616     EISSN: 15217035     Source Type: Journal    
DOI: 10.1016/j.clim.2011.10.001     Document Type: Article

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