Congenital CNS hypomyelination in the Fig4 null mouse is rescued by neuronal expression of the PI(3,5)P 2 phosphatase Fig4

Journal of Neuroscience

Volumn 31, Issue 48, 2011, Pages 17736-17751

  Winters, Jesse J ^a   Ferguson, Cole J ^a   Lenk, Guy M ^a   Giger Mateeva, Vessela I ^b   Shrager, Peter ^c   Meisler, Miriam H ^a,b   Giger, Roman J ^a,b  

^a UNIVERSITY OF MICHIGAN   (United States)

^b UNIVERSITY OF MICHIGAN MEDICAL SCHOOL   (United States)

^c UNIVERSITY OF ROCHESTER MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MUTANT PROTEIN; MYELIN; PHOSPHATIDYLINOSITOL; PHOSPHATIDYLINOSITOL 3,5-BISPHOSPHATE PHOSPHATASE; UNCLASSIFIED DRUG;

ACTION POTENTIAL; ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN; CELL DEATH; CONGENITAL DISORDER; CONTROLLED STUDY; ELECTRON MICROSCOPY; FIG4 GENE; GENE; HEREDITARY MOTOR SENSORY NEUROPATHY; HISTOCHEMISTRY; IMMUNOFLUORESCENCE; MISSENSE MUTATION; MOUSE; MYELIN DEFICIENCY; MYELINATION; NERVE CONDUCTION; NONHUMAN; NULL ALLELE; OLIGODENDROGLIA; OPTIC NERVE; PRIORITY JOURNAL; PROTEIN EXPRESSION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SPINAL CORD; TREMOR; WESTERN BLOTTING;

ANIMALS; AXONS; CHARCOT-MARIE-TOOTH DISEASE; FLAVOPROTEINS; MICE; MICE, TRANSGENIC; MYELIN SHEATH; NERVE FIBERS, MYELINATED; NEURONS; PHOSPHATIDYLINOSITOLS; PHOSPHORIC MONOESTER HYDROLASES;

EID: 82555200841     PISSN: 02706474     EISSN: 15292401     Source Type: Journal    
DOI: 10.1523/JNEUROSCI.1482-11.2011     Document Type: Article

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