Mortality risk of untreated myosin-binding protein crelated hypertrophic cardiomyopathy: Insight into the natural history

Journal of the American College of Cardiology

Volumn 58, Issue 23, 2011, Pages 2406-2414

  Nannenberg, Eline A ^a   Michels, Michelle ^b   Christiaans, Imke ^a   Majoor Krakauer, Danielle ^b   Hoedemaekers, Yvonne M ^b   Van Tintelen, J Peter ^c   Lombardi, M Paola ^a   Ten Cate, Folkert J ^b   Schinkel, Arend F L ^b,c   Tijssen, Jan G P ^c   Van Langen, Irene M ^c   Wilde, Arthur A M ^a   Sijbrands, Eric J G ^b  

^a ACADEMIC MEDICAL CENTER   (Netherlands)

^b ERASMUS MEDICAL CENTER   (Netherlands)

^c UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

Author keywords

family tree mortality ratio method; hypertrophic cardiomyopathy; mortality; myosin binding protein C gene; natural history

Indexed keywords

MYOSIN BINDING PROTEIN C;

ADULT; AGE DISTRIBUTION; ARTICLE; CHILD; COHORT ANALYSIS; CONTROLLED STUDY; DISEASE COURSE; FEMALE; FRAMESHIFT MUTATION; GENE; GENE MUTATION; GENEALOGY; GENETIC ASSOCIATION; GENETIC SCREENING; HUMAN; HYPERTROPHIC CARDIOMYOPATHY; MAJOR CLINICAL STUDY; MALE; MORTALITY; MYOSIN BINDING PROTEIN C GENE; OUTCOME ASSESSMENT; PEDIGREE ANALYSIS; PRIORITY JOURNAL; RELATIVE; SCHOOL CHILD; STANDARDIZED MORTALITY RATIO; SUDDEN DEATH; TRUNCATING MUTATION;

ADOLESCENT; ADULT; AGE DISTRIBUTION; AGED; AGED, 80 AND OVER; CARDIOMYOPATHY, HYPERTROPHIC; CARRIER PROTEINS; CHILD; CHILD, PRESCHOOL; FEMALE; FOLLOW-UP STUDIES; GENETIC PREDISPOSITION TO DISEASE; HUMANS; INFANT; MALE; MIDDLE AGED; MYOSINS; PEDIGREE; PROGNOSIS; RETROSPECTIVE STUDIES; RISK ASSESSMENT; SURVIVAL RATE; TIME FACTORS; YOUNG ADULT;

EID: 81855225288     PISSN: 07351097     EISSN: 15583597     Source Type: Journal    
DOI: 10.1016/j.jacc.2011.07.044     Document Type: Article

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