Integrins (α7β1) in muscle function and survival disrupted expression in merosin-deficient congenital muscular dystrophy

Journal of Clinical Investigation

Volumn 100, Issue 7, 1997, Pages 1870-1881

  Vachon, Pierre H ^a   Xu, Hong ^a   Liu, Ling ^a,b   Loechel, Frosty ^c   Hayashi, Yukiko ^d   Arahata, Kiichi ^d   Reed, John C ^a   Wewer, Ulla M ^c   Engvall, Eva ^a  

^a BURNHAM INSTITUTE   (United States)

^b STOCKHOLM UNIVERSITY   (Sweden)

^c UNIVERSITY OF COPENHAGEN   (Denmark)

^d NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

Author keywords

Apoptosis; Basement membrane; Dystrophin glycoprotein complex; Extracellular matrix; Laminin receptor

Indexed keywords

DYSTROPHIN; INTEGRIN; LAMININ; LAMININ RECEPTOR; PROTEOGLYCAN; UTROPHIN; BETA1 INTEGRIN; CYTOSKELETON PROTEIN; INTEGRIN ALPHA7BETA1; MEMBRANE PROTEIN;

ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; BASEMENT MEMBRANE; CELL SURVIVAL; CELLULAR DISTRIBUTION; CONTROLLED STUDY; ETIOLOGY; EXTRACELLULAR MATRIX; GENE MUTATION; HUMAN; HUMAN CELL; HUMAN TISSUE; MOUSE; MUSCLE CELL; MUSCLE FUNCTION; MUSCULAR DYSTROPHY; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; ANIMAL; ANIMAL MUSCULAR DYSTROPHY; BIOSYNTHESIS; C57BL MOUSE; CELL DIFFERENTIATION; GENETICS; HAMSTER; IMMUNOHISTOCHEMISTRY; METABOLISM; MOUSE MUTANT; PHYSIOLOGY; SARCOLEMMA; SKELETAL MUSCLE; TISSUE DISTRIBUTION; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE;

ANIMALS; ANTIGENS, CD29; CELL DIFFERENTIATION; CELL SURVIVAL; CRICETINAE; CYTOSKELETAL PROTEINS; DYSTROPHIN; HUMANS; IMMUNOHISTOCHEMISTRY; INTEGRINS; LAMININ; MEMBRANE GLYCOPROTEINS; MICE; MICE, INBRED C57BL; MICE, INBRED MDX; MICE, MUTANT STRAINS; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; MUSCULAR DYSTROPHY, ANIMAL; RECEPTORS, LAMININ; SARCOLEMMA; TISSUE DISTRIBUTION;

EID: 0030610576     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI119716     Document Type: Article

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