Quaternary organization of GPIb-IX complex and insights into Bernard-Soulier syndrome revealed by the structures of GPIβ and a GPIβ/GPIX chimera

Blood

Volumn 118, Issue 19, 2011, Pages 5292-5301

  McEwan, Paul A ^a   Yang, Wenjun ^b   Carr, Katherine H ^a   Mo, Xi ^b   Zheng, Xiaofeng ^b   Li, Renhao ^b,c   Emsley, Jonas ^a  

^a UNIVERSITY OF NOTTINGHAM   (United Kingdom)

^b UNIVERSITY OF TEXAS MEDICAL SCHOOL   (United States)

^c EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

DISULFIDE; PROTEIN GPIB BETA; PROTEIN GPIX; TETRAMER; THROMBIN RECEPTOR; TYROSINE; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; ARTICLE; BERNARD SOULIER DISEASE; CARBOXY TERMINAL SEQUENCE; CHIMERA; CRYSTALLIZATION; DISULFIDE BOND; HUMAN; LEUCINE RICH REPEAT; MISSENSE MUTATION; MUTAGENESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN PROTEIN INTERACTION; PROTEIN QUATERNARY STRUCTURE; PROTEIN SECRETION; PROTEIN STRUCTURE; X RAY CRYSTALLOGRAPHY;

EID: 81055141756     PISSN: 00064971     EISSN: 15280020     Source Type: Journal    
DOI: 10.1182/blood-2011-05-356253     Document Type: Article

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