Lipid composition of whole brain and cerebellum in hurler syndrome (MPS IH) mice

Neurochemical Research

Volumn 36, Issue 9, 2011, Pages 1669-1676

  Heinecke, Karie A ^a   Peacock, Brandon N ^b   Blazar, Bruce R ^b   Tolar, Jakub ^b   Seyfried, Thomas N ^a  

^a BOSTON COLLEGE   (United States)

^b UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

Author keywords

Gangliosides; GD3; Hurler syndrome; Lipids; Mouse model; MPS IH

Indexed keywords

GANGLIOSIDE GD3; GANGLIOSIDE GM2; GANGLIOSIDE GM3; SIALIC ACID;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN; CEREBELLUM; CONTROLLED STUDY; HURLER SYNDROME; LIPID COMPOSITION; LIPID STORAGE; MOUSE; NERVE DEGENERATION; NONHUMAN; PRIORITY JOURNAL; TISSUE DISTRIBUTION;

ANIMALS; BRAIN CHEMISTRY; CEREBELLUM; DISEASE MODELS, ANIMAL; FEMALE; GANGLIOSIDES; GLYCOSAMINOGLYCANS; HUMANS; IDURONIDASE; LIPID METABOLISM; LIPIDS; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MUCOPOLYSACCHARIDOSIS I;

MUS;

EID: 80755172140     PISSN: 03643190     EISSN: 15736903     Source Type: Journal    
DOI: 10.1007/s11064-011-0400-y     Document Type: Article

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