Murine mucopolysaccharidosis type I: Targeted disruption of the murine α-L-iduronidase gene

Human Molecular Genetics

Volumn 6, Issue 4, 1997, Pages 503-511

  Clarke, Lorne A ^a   Russell, Christopher S ^a   Pownall, Scott ^a   Warrington, Cara L ^a   Borowski, Anita ^a   Dimmick, James E ^a   Toone, Jennifer ^a   Jirik, Frank R ^a  

^a UNIVERSITY OF BRITISH COLUMBIA   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

GLYCOSAMINOGLYCAN; LEVO IDURONIDASE;

ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CARTILAGE CELL; ENZYME ACTIVITY; FEMALE; GENE MUTATION; GENE THERAPY; GLIA CELL; HURLER SYNDROME; KIDNEY TUBULE CELL; KUPFFER CELL; LIVER CELL; LYSOSOME STORAGE DISEASE; MALE; MOUSE; MUCOPOLYSACCHARIDOSIS; NERVE CELL; NEWBORN; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RADIOGRAPHY; RETICULOENDOTHELIAL SYSTEM; SPLEEN;

ABNORMALITIES, MULTIPLE; ANIMALS; BLOTTING, NORTHERN; BLOTTING, SOUTHERN; CLONING, MOLECULAR; DISEASE MODELS, ANIMAL; FACIES; GENE EXPRESSION; GENE TARGETING; GLYCOSAMINOGLYCANS; IDURONIDASE; LIVER; MICE; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; MUCOPOLYSACCHARIDOSIS I; PHENOTYPE; SPLEEN;

ANIMALIA; MURINAE;

EID: 0030899669     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/6.4.503     Document Type: Article

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