Npc1 deficiency in the C57BL/6J genetic background enhances Niemann-Pick disease type C spleen pathology

Biochemical and Biophysical Research Communications

Volumn 413, Issue 3, 2011, Pages 400-406

  Parra, Julio ^a   Klein, Andrés D ^a   Castro, Juan ^a   Morales, María Gabriela ^a   Mosqueira, Matías ^a   Valencia, Ilse ^a   Cortés, Victor ^a   Rigotti, Attilio ^a   Zanlungo, Silvana ^a  

^a PONTIFICIA UNIVERSIDAD CATÓLICA DE CHILE   (Chile)

Author keywords

Cholesterol; Liver; Niemann Pick type C disease; NPC1; Spleen

Indexed keywords

CHOLESTEROL; PHOSPHOLIPID;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; DISEASE COURSE; ERYTHROCYTE DISORDER; FOAM CELL; GENE MUTATION; GENETIC ANALYSIS; HEMOGLOBIN DETERMINATION; LEUKOCYTE; LIFESPAN; MOUSE; MOUSE STRAIN; NIEMANN PICK DISEASE; NONHUMAN; ORGAN WEIGHT; PRIORITY JOURNAL;

ANIMALS; BLOOD PLATELETS; DISEASE PROGRESSION; ERYTHROCYTES; LONGEVITY; MICE; MICE, INBRED BALB C; MICE, INBRED C57BL; MICE, MUTANT STRAINS; MUTATION; NIEMANN-PICK DISEASE, TYPE C; ORGAN SIZE; PROTEINS; SPLEEN;

MUS;

EID: 80053299096     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2011.08.096     Document Type: Article

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