-
1
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
J.R. Riordan, J.M. Rommens, B. Kerem, N. Alon, R. Rozmahel, Z. Grzelczak, J. Zielenski, S. Lok, N. Plavsic, J.L. Chou, M.L. Drumm, M.C. Iannuzzi, F.S. Collins, and L.-C. Tsui Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA Science 245 1989 1066 1073 (Pubitemid 19231814)
-
(1989)
Science
, vol.245
, Issue.4922
, pp. 1066-1073
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.-S.3
Alon, N.4
Rozmahel, R.5
Grzelczak, Z.6
Zielinski, J.7
Lok, S.8
Plavsic, N.9
Chou, J.-L.10
Drumm, M.L.11
Iannuzzi, M.C.12
Collins, F.S.13
Tsui, L.-C.14
-
2
-
-
0025868103
-
Demonstration that CFTR is a chloride channel by alteration of its anion selectivity
-
M.P. Anderson, R.J. Gregory, S. Thompson, D.W. Souza, S. Paul, R.C. Mulligan, A.E. Smith, and M.J. Welsh Demonstration that CFTR is a chloride channel by alteration of its anion selectivity Science 253 1991 202 205 (Pubitemid 21917143)
-
(1991)
Science
, vol.253
, Issue.5016
, pp. 202-205
-
-
Anderson, M.P.1
Gregory, R.J.2
Thompson, S.3
Souza, D.W.4
Paul, S.5
Mulligan, R.C.6
Smith, A.E.7
Welsh, M.J.8
-
3
-
-
0034695758
-
Interleukin-1β regulates CFTR expression in human intestinal T84 cells
-
DOI 10.1016/S0925-4439(99)00105-2, PII S0925443999001052
-
E.G. Cafferata, A.M. Gonzalez-Guerrico, L. Giordano, O.H. Pivetta, and T.A. Santa-Coloma Interleukin-1β regulates CFTR expression in human intestinal T84 cells Biochim. Biophys. Acta 1500 2000 241 248 (Pubitemid 30060396)
-
(2000)
Biochimica et Biophysica Acta - Molecular Basis of Disease
, vol.1500
, Issue.2
, pp. 241-248
-
-
Cafferata, E.G.1
Gonzalez-Guerrico, A.M.2
Giordano, L.3
Pivetta, O.H.4
Santa-Coloma, T.A.5
-
4
-
-
37049008442
-
CISD1 codifies a mitochondrial protein upregulated by the CFTR channel
-
DOI 10.1016/j.bbrc.2007.11.076, PII S0006291X07024849
-
G.L. Taminelli, V. Sotomayor, A.G. Valdivieso, M.L. Teiber, M.C. Marin, and T.A. Santa-Coloma CISD1 codifies a mitochondrial protein upregulated by the CFTR channel Biochem. Biophys. Res. Commun. 365 2008 856 862 (Pubitemid 350245381)
-
(2008)
Biochemical and Biophysical Research Communications
, vol.365
, Issue.4
, pp. 856-862
-
-
Taminelli, G.L.1
Sotomayor, V.2
Valdivieso, A.G.3
Teiber, M.L.4
Marin, M.C.5
Santa-Coloma, T.A.6
-
5
-
-
33947644153
-
The expression of the mitochondrial gene MT-ND4 is downregulated in cystic fibrosis
-
DOI 10.1016/j.bbrc.2007.03.057, PII S0006291X07005384
-
A.G. Valdivieso, F. Marcucci, G. Taminelli, A.G. Guerrico, S. Alvarez, M.L. Teiber, M.A. Dankert, and T.A. Santa-Coloma The expression of the mitochondrial gene MT-ND4 is downregulated in cystic fibrosis Biochem. Biophys. Res. Commun. 356 2007 805 809 (Pubitemid 46499038)
-
(2007)
Biochemical and Biophysical Research Communications
, vol.356
, Issue.3
, pp. 805-809
-
-
Valdivieso, A.G.1
Marcucci, F.2
Taminelli, G.3
Guerrico, A.G.4
Alvarez, S.5
Teiber, M.L.6
Dankert, M.A.7
Santa-Coloma, T.A.8
-
6
-
-
0026919711
-
Human cystic fibrosis transmembrane conductance regulator directed to respiratory epithelial cells of transgenic mice
-
J.A. Whitsett, C.R. Dey, B.R. Stripp, K.A. Wikenheiser, J.C. Clark, S.E. Wert, R.J. Gregory, A.E. Smith, J.A. Cohn, J.M. Wilson, and J. Engelhardt Human cystic fibrosis transmembrane conductance regulator directed to respiratory epithelial cells of transgenic mice Nat. Genet. 2 1992 13 20
-
(1992)
Nat. Genet.
, vol.2
, pp. 13-20
-
-
Whitsett, J.A.1
Dey, C.R.2
Stripp, B.R.3
Wikenheiser, K.A.4
Clark, J.C.5
Wert, S.E.6
Gregory, R.J.7
Smith, A.E.8
Cohn, J.A.9
Wilson, J.M.10
Engelhardt, J.11
-
8
-
-
0026148375
-
A cystic fibrosis bronchial epithelial cell line: Immortalization by adeno-12-SV40 infection
-
P.L. Zeitlin, L. Lu, J. Rhim, G. Cutting, G. Stetten, K.A. Kieffer, R. Craig, and W.B. Guggino A cystic fibrosis bronchial epithelial cell line: immortalization by adeno-12-SV40 infection Am. J. Respir. Cell Mol. Biol. 4 1991 313 319
-
(1991)
Am. J. Respir. Cell Mol. Biol.
, vol.4
, pp. 313-319
-
-
Zeitlin, P.L.1
Lu, L.2
Rhim, J.3
Cutting, G.4
Stetten, G.5
Kieffer, K.A.6
Craig, R.7
Guggino, W.B.8
-
9
-
-
0028980536
-
CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP
-
E.M. Schwiebert, M.E. Egan, T.H. Hwang, S.B. Fulmer, S.S. Allen, G.R. Cutting, and W.B. Guggino CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP Cell 81 1995 1063 1073
-
(1995)
Cell
, vol.81
, pp. 1063-1073
-
-
Schwiebert, E.M.1
Egan, M.E.2
Hwang, T.H.3
Fulmer, S.B.4
Allen, S.S.5
Cutting, G.R.6
Guggino, W.B.7
-
11
-
-
0026325533
-
Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation
-
W. Dalemans, P. Barbry, G. Champigny, S. Jallat, K. Dott, D. Dreyer, R.G. Crystal, A. Pavirani, J.P. Lecocq, and M. Lazdunski Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation Nature 354 1991 526 528 (Pubitemid 21896832)
-
(1991)
Nature
, vol.354
, Issue.6354
, pp. 526-528
-
-
Dalemans, W.1
Barbryt, P.2
Champigny, G.3
Jallat, S.4
Dott, K.5
Dreyer, D.6
Crystal, R.G.7
Pavirani, A.8
Lecocq, J.-P.9
Lazdunski, M.10
-
14
-
-
0023123058
-
Membrane chloride transport measured using a chloride-sensitive fluorescent probe
-
DOI 10.1021/bi00379a002
-
N.P. Illsley, and A.S. Verkman Membrane chloride transport measured using a chloride-sensitive fluorescent probe Biochemistry 26 1987 1215 1219 (Pubitemid 17045847)
-
(1987)
Biochemistry
, vol.26
, Issue.5
, pp. 1215-1219
-
-
Illsley, N.P.1
Verkman, A.S.2
-
15
-
-
0032715502
-
Long-wavelength iodide-sensitive fluorescent indicators for measurement of functional CFTR expression in cells
-
S. Jayaraman, L. Teitler, B. Skalski, and A.S. Verkman Long-wavelength iodide-sensitive fluorescent indicators for measurement of functional CFTR expression in cells Am. J. Physiol. 277 1999 C1008 C1018
-
(1999)
Am. J. Physiol.
, vol.277
-
-
Jayaraman, S.1
Teitler, L.2
Skalski, B.3
Verkman, A.S.4
-
16
-
-
0025032271
-
Development and biological applications of chloride-sensitive fluorescent indicators
-
A.S. Verkman Development and biological applications of chloride-sensitive fluorescent indicators Am. J. Physiol. 259 1990 C375 C388 (Pubitemid 20317750)
-
(1990)
American Journal of Physiology - Cell Physiology
, vol.259
, Issue.3
-
-
Verkman, A.S.1
-
17
-
-
0029896163
-
Regulation, substrates, and functions of Src
-
M.T. Brown, and J.A. Cooper Regulation, substrates, and functions of Src Biochim. Biophys. Acta 1287 1996 121 149
-
(1996)
Biochim. Biophys. Acta
, vol.1287
, pp. 121-149
-
-
Brown, M.T.1
Cooper, J.A.2
-
18
-
-
0025987020
-
Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel
-
S.H. Cheng, D.P. Rich, J. Marshall, R.J. Gregory, M.J. Welsh, and A.E. Smith Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel Cell 66 1991 1027 1036 (Pubitemid 121001734)
-
(1991)
Cell
, vol.66
, Issue.5
, pp. 1027-1036
-
-
Cheng, S.H.1
Rich, D.P.2
Marshall, J.3
Gregory, R.J.4
Welsh, M.J.5
Smith, A.E.6
-
19
-
-
0025155528
-
Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells
-
D.P. Rich, M.P. Anderson, R.J. Gregory, S.H. Cheng, S. Paul, D.M. Jefferson, J.D. McCann, K.W. Klinger, A.E. Smith, and M.J. Welsh Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells Nature 347 1990 358 363
-
(1990)
Nature
, vol.347
, pp. 358-363
-
-
Rich, D.P.1
Anderson, M.P.2
Gregory, R.J.3
Cheng, S.H.4
Paul, S.5
Jefferson, D.M.6
McCann, J.D.7
Klinger, K.W.8
Smith, A.E.9
Welsh, M.J.10
-
20
-
-
0025807911
-
CAMP-inducible chloride conductance in mouse fibroblast lines stably expressing the human cystic fibrosis transmembrane conductance regulator
-
J.M. Rommens, S. Dho, C.E. Bear, N. Kartner, D. Kennedy, J.R. Riordan, L.C. Tsui, and J.K. Foskett CAMP-inducible chloride conductance in mouse fibroblast lines stably expressing the human cystic fibrosis transmembrane conductance regulator Proc. Natl. Acad. Sci. USA 88 1991 7500 7504 (Pubitemid 21915180)
-
(1991)
Proceedings of the National Academy of Sciences of the United States of America
, vol.88
, Issue.17
, pp. 7500-7504
-
-
Rommens, J.M.1
Dho, S.2
Bear, C.E.3
Kartner, N.4
Kennedy, D.5
Riordan, J.R.6
Tsui, L.-C.7
Foskett, J.K.8
-
21
-
-
0036840749
-
Normal function of the cystic fibrosis conductance regulator protein can be associated with homozygous ΔF508 mutation
-
DOI 10.1203/01.PDR.0000032981.64413.AD
-
I. Sermet-Gaudelus, B. Vallee, I. Urbin, T. Torossi, R. Marianovski, A. Fajac, M.N. Feuillet, J.L. Bresson, G. Lenoir, J.F. Bernaudin, and A. Edelman Normal function of the cystic fibrosis conductance regulator protein can be associated with homozygous ΔF508 mutation Pediatr. Res. 52 2002 628 635 (Pubitemid 35286028)
-
(2002)
Pediatric Research
, vol.52
, Issue.5
, pp. 628-635
-
-
Sermet-Gaudelus, I.1
Vallee, B.2
Urbin, I.3
Torossi, T.4
Marianovski, R.5
Fajac, A.6
Feuillet, M.-N.7
Bresson, J.-L.8
Lenoir, G.9
Bernaudin, J.F.10
Edelman, A.11
-
22
-
-
2542626706
-
Reversal of cystic fibrosis phenotype in a cultured Δ508 cystic fibrosis, transmembrane conductance regulator cell line by oligonucleotide insertion
-
DOI 10.1073/pnas.0401933101
-
P.C. Zamecnik, M.K. Raychowdhury, D.R. Tabatadze, and H.F. Cantiello Reversal of cystic fibrosis phenotype in a cultured Δ508 cystic fibrosis transmembrane conductance regulator cell line by oligonucleotide insertion Proc. Natl. Acad. Sci. USA 101 2004 8150 8155 (Pubitemid 38698069)
-
(2004)
Proceedings of the National Academy of Sciences of the United States of America
, vol.101
, Issue.21
, pp. 8150-8155
-
-
Zamecnik, P.C.1
Raychowdhury, M.K.2
Tabatadze, D.R.3
Cantiello, H.F.4
-
23
-
-
0347989353
-
Halide fluxes in epithelial cells measured with an automated cell plate reader
-
DOI 10.1016/S0003-2697(03)00142-8
-
D.A. Mahlangu, and J.A. Dix Halide fluxes in epithelial cells measured with an automated cell plate reader Anal. Biochem. 325 2004 28 34 (Pubitemid 38050263)
-
(2004)
Analytical Biochemistry
, vol.325
, Issue.1
, pp. 28-34
-
-
Mahlangu, D.A.F.D.1
Dix, J.A.2
-
24
-
-
0030798074
-
A flow cytometric method for measurement of intracellular chloride concentration in lymphocytes using the halide-specific probe 6-methoxy-N-(3- sulfopropyl) quinolinium (SPQ)
-
DOI 10.1002/(SICI)1097-0320(19970801)28:4<316::AID-CYTO7>3.0.CO;2-9
-
B. Pilas, and G. Durack A flow cytometric method for measurement of intracellular chloride concentration in lymphocytes using the halide-specific probe 6-methoxy-N-(3-sulfopropyl)quinolinium (SPQ) Cytometry 28 1997 316 322 (Pubitemid 27359608)
-
(1997)
Cytometry
, vol.28
, Issue.4
, pp. 316-322
-
-
Pilas, B.1
Durack, G.2
-
25
-
-
0024832189
-
Fluorescence measurement of chloride transport in monolayer cultured cells. Mechanisms of chloride transport in fibroblasts
-
A.C. Chao, J.A. Dix, M.C. Sellers, and A.S. Verkman Fluorescence measurement of chloride transport in monolayer cultured cells: mechanisms of chloride transport in fibroblasts Biophys. J. 56 1989 1071 1081 (Pubitemid 20017623)
-
(1989)
Biophysical Journal
, vol.56
, Issue.6
, pp. 1071-1081
-
-
Chao, A.C.1
Dix, J.A.2
Sellers, M.C.3
Verkman, A.S.4
-
26
-
-
0023918379
-
Estimation of intracellular chloride activity in isolated perfused rabbit proximal convoluted tubules using a fluorescent indicator
-
R. Krapf, C.A. Berry, and A.S. Verkman Estimation of intracellular chloride activity in isolated perfused rabbit proximal convoluted tubules using a fluorescent indicator Biophys. J. 53 1988 955 962
-
(1988)
Biophys. J.
, vol.53
, pp. 955-962
-
-
Krapf, R.1
Berry, C.A.2
Verkman, A.S.3
-
27
-
-
0033372495
-
Aspirin and some other nonsteroidal anti-inflammatory drugs inhibit cystic fibrosis transmembrane conductance regulator protein gene expression in T-84 cells
-
DOI 10.1080/09629359990388
-
D. Tondelier, F. Brouillard, J. Lipecka, R. Labarthe, M. Bali, M.A. Costa de Beauregard, T. Torossi, M. Cougnon, A. Edelman, and M. Baudouin-Legros Aspirin and some other nonsteroidal anti-inflammatory drugs inhibit cystic fibrosis transmembrane conductance regulator protein gene expression in T-84 cells Mediat. Inflamm. 8 1999 219 227 (Pubitemid 30019332)
-
(1999)
Mediators of Inflammation
, vol.8
, Issue.4-5
, pp. 219-227
-
-
Tondelier, D.1
Brouillard, F.2
Lipecka, J.3
Labarthe, R.4
Bali, M.5
Costa De Beauregard, M.-A.6
Torossi, T.7
Cougnon, M.8
Edelman, A.9
Baudouin-Legros, M.10
-
28
-
-
0036896008
-
Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion
-
DOI 10.1172/JCI200216112
-
T. Ma, J.R. Thiagarajah, H. Yang, N.D. Sonawane, C. Folli, L.J. Galietta, and A.S. Verkman Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion J. Clin. Invest. 110 2002 1651 1658 (Pubitemid 35424243)
-
(2002)
Journal of Clinical Investigation
, vol.110
, Issue.11
, pp. 1651-1658
-
-
Ma, T.1
Thiagarajah, J.R.2
Yang, H.3
Sonawane, N.D.4
Folli, C.5
Galietta, L.J.V.6
Verkman, A.S.7
-
29
-
-
3242674162
-
TGFβ down-regulation of the CFTR: A means to limit epithelial chloride secretion
-
DOI 10.1016/j.yexcr.2004.04.026, PII S0014482704002423
-
K.L. Howe, A. Wang, M.M. Hunter, B.A. Stanton, and D.M. McKay TGFβ down-regulation of the CFTR: a means to limit epithelial chloride secretion Exp. Cell Res. 298 2004 473 484 (Pubitemid 38950864)
-
(2004)
Experimental Cell Research
, vol.298
, Issue.2
, pp. 473-484
-
-
Howe, K.L.1
Wang, A.2
Hunter, M.M.3
Stanton, B.A.4
McKay, D.M.5
-
30
-
-
0025248420
-
The T84 human colonic adenocarcinoma cell line produces mucin in culture and releases it in response to various secretagogues
-
D.J. McCool, M.A. Marcon, J.F. Forstner, and G.G. Forstner The T84 human colonic adenocarcinoma cell line produces mucin in culture and releases it in response to various secretagogues Biochem. J. 267 1990 491 500 (Pubitemid 20136086)
-
(1990)
Biochemical Journal
, vol.267
, Issue.2
, pp. 491-500
-
-
McCool, D.J.1
Marcon, M.A.2
Forstner, J.F.3
Forstner, G.G.4
-
31
-
-
0037016669
-
The chloride channel ClC-4 co-localizes with cystic fibrosis transmembrane conductance regulator and may mediate chloride flux across the apical membrane of intestinal epithelia
-
DOI 10.1074/jbc.M106968200
-
R. Mohammad-Panah, C. Ackerley, J. Rommens, M. Choudhury, Y. Wang, and C.E. Bear The chloride channel ClC-4 co-localizes with cystic fibrosis transmembrane conductance regulator and may mediate chloride flux across the apical membrane of intestinal epithelia J. Biol. Chem. 277 2002 566 574 (Pubitemid 34952093)
-
(2002)
Journal of Biological Chemistry
, vol.277
, Issue.1
, pp. 566-574
-
-
Mohammad-Panah, R.1
Ackerley, C.2
Rommens, J.3
Choudhury, M.4
Wang, Y.5
Bear, C.E.6
-
32
-
-
0035896522
-
ClC-2 contributes to native chloride secretion by a human intestinal cell line, Caco-2
-
R. Mohammad-Panah, K. Gyomorey, J. Rommens, M. Choudhury, C. Li, Y. Wang, and C.E. Bear ClC-2 contributes to native chloride secretion by a human intestinal cell line, Caco-2 J. Biol. Chem. 276 2001 8306 8313
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 8306-8313
-
-
Mohammad-Panah, R.1
Gyomorey, K.2
Rommens, J.3
Choudhury, M.4
Li, C.5
Wang, Y.6
Bear, C.E.7
-
33
-
-
0027312715
-
Mechanism of inhibition of cAMP-dependent epithelial chloride secretion by phorbol esters
-
B.Q. Shen, R.A. Barthelson, W. Skach, D.C. Gruenert, E. Sigal, R.J. Mrsny, and J.H. Widdicombe Mechanism of inhibition of cAMP-dependent epithelial chloride secretion by phorbol esters J. Biol. Chem. 268 1993 19070 19075 (Pubitemid 23273862)
-
(1993)
Journal of Biological Chemistry
, vol.268
, Issue.25
, pp. 19070-19075
-
-
Shen, B.-Q.1
Barthelson, R.A.2
Skach, W.3
Gruenert, D.C.4
Sigal, E.5
Mrsny, R.J.6
Widdicombe, J.H.7
-
34
-
-
11044222421
-
Transepithelial fluctuation analysis of chloride secretion
-
DOI 10.1016/j.jcf.2004.05.027, PII S1569199304000815
-
A.K. Singh, B.D. Schultz, W. van Driessche, and R.J. Bridges Transepithelial fluctuation analysis of chloride secretion J. Cyst. Fibros. 3 Suppl. 2 2004 127 132 (Pubitemid 40045584)
-
(2004)
Journal of Cystic Fibrosis
, vol.3
, Issue.SUPPL. 2
, pp. 127-132
-
-
Singh, A.K.1
Schultz, B.D.2
Van Driessche, W.3
Bridges, R.J.4
-
35
-
-
0025020683
-
Chloride conductive and cotransport mechanisms in cultures of canine tracheal epithelial cells measured by an entrapped fluorescent indicator
-
A.C. Chao, J.H. Widdicombe, and A.S. Verkman Chloride conductive and cotransport mechanisms in cultures of canine tracheal epithelial cells measured by an entrapped fluorescent indicator J. Membr. Biol. 113 1990 193 202 (Pubitemid 20070317)
-
(1990)
Journal of Membrane Biology
, vol.113
, Issue.3
, pp. 193-202
-
-
Chao, A.C.1
Widdicombe, J.H.2
Verkman, A.S.3
-
36
-
-
0028326344
-
Regulated Cl transport, K and Cl permeability, and exocytosis in T84 cells
-
M.E. Huflejt, R.A. Blum, S.G. Miller, H.P. Moore, and T.E. Machen Regulated Cl transport, K and Cl permeability, and exocytosis in T84 cells J. Clin. Invest. 93 1994 1900 1910 (Pubitemid 24143067)
-
(1994)
Journal of Clinical Investigation
, vol.93
, Issue.5
, pp. 1900-1910
-
-
Huflejt, M.E.1
Blum, R.A.2
Miller, S.G.3
Moore, H.-P.H.4
Machen, T.E.5
-
37
-
-
0031836774
-
- channels using the halide- sensitive fluorescent indicator 6-methoxy-N-(3-sulfopropyl)quinolinium
-
- channels using the halide-sensitive fluorescent indicator 6-methoxy-N-(3-sulfopropyl)quinolinium Biophys. J. 75 1998 115 123 (Pubitemid 28311801)
-
(1998)
Biophysical Journal
, vol.75
, Issue.1
, pp. 115-123
-
-
Srinivas, S.P.1
Bonanno, J.A.2
Hughes, B.A.3
|