-
1
-
-
0028937612
-
Relationship between transfusion regimen and suppression of erythropoiesis in betathalassaemia major
-
Cazzola M, De Stefano P, Ponchio L, Locatelli F, Beguin Y, Dessi C, et al. Relationship between transfusion regimen and suppression of erythropoiesis in betathalassaemia major. Br J Haematol 1995;89:473-8.
-
(1995)
Br J Haematol
, vol.89
, pp. 473-478
-
-
Cazzola, M.1
de Stefano, P.2
Ponchio, L.3
Locatelli, F.4
Beguin, Y.5
Dessi, C.6
-
2
-
-
0031041962
-
A moderate transfusion regimen may reduce iron loading in beta-thalassemia major without producing excessive expansion of erythropoiesis
-
Cazzola M, Borgna-Pignatti C, Locatelli F, Ponchio L, Beguin Y, De Stefano P. A moderate transfusion regimen may reduce iron loading in beta-thalassemia major without producing excessive expansion of erythropoiesis. Transfusion 1997;37:135-40.
-
(1997)
Transfusion
, vol.37
, pp. 135-140
-
-
Cazzola, M.1
Borgna-Pignatti, C.2
Locatelli, F.3
Ponchio, L.4
Beguin, Y.5
de Stefano, P.6
-
3
-
-
0035725868
-
Practical management of iron overload
-
Porter JB. Practical management of iron overload. Br J Haematol 2001;115:239-52.
-
(2001)
Br J Haematol
, vol.115
, pp. 239-252
-
-
Porter, J.B.1
-
4
-
-
0019349312
-
Clinical consequences of acquired transfusional iron overload in adults
-
Schafer AI, Cheron RG, Dluhy R, Cooper B, Gleason RE, Soeldner JS, et al. Clinical consequences of acquired transfusional iron overload in adults. N Engl J Med 1981;304:319-24.
-
(1981)
N Engl J Med
, vol.304
, pp. 319-324
-
-
Schafer, A.I.1
Cheron, R.G.2
Dluhy, R.3
Cooper, B.4
Gleason, R.E.5
Soeldner, J.S.6
-
5
-
-
0033599057
-
Disorders of iron metabolism
-
Andrews NC. Disorders of iron metabolism. N Engl J Med 1999;341:1986-95.
-
(1999)
N Engl J Med
, vol.341
, pp. 1986-1995
-
-
Andrews, N.C.1
-
6
-
-
0031876331
-
Survival and disease complications in thalassemia major
-
Borgna-Pignatti C, Rugolotto S, De Stefano P, Piga A, Di Gregorio F, Gamberini MR, et al. Survival and disease complications in thalassemia major. Ann N Y Acad Sci 1998;850:227-31.
-
(1998)
Ann N Y Acad Sci
, vol.850
, pp. 227-231
-
-
Borgna-Pignatti, C.1
Rugolotto, S.2
de Stefano, P.3
Piga, A.4
di Gregorio, F.5
Gamberini, M.R.6
-
7
-
-
0024337363
-
Survival and causes of death in thalassaemia major
-
Zurlo MG, De Stefano P, Borgna-Pignatti C, Di Palma A, Piga A, Melevendi C, et al. Survival and causes of death in thalassaemia major. Lancet 1989;2:27-30.
-
(1989)
Lancet
, vol.2
, pp. 27-30
-
-
Zurlo, M.G.1
de Stefano, P.2
Borgna-Pignatti, C.3
di Palma, A.4
Piga, A.5
Melevendi, C.6
-
8
-
-
0035383809
-
Cardiac involvement in thalassemia intermedia: A multicenter study
-
Aessopos A, Farmakis D, Karagiorga M, Voskaridou E, Loutradi A, Hatziliami A, et al. Cardiac involvement in thalassemia intermedia: a multicenter study. Blood 2001;97:3411-6.
-
(2001)
Blood
, vol.97
, pp. 3411-3416
-
-
Aessopos, A.1
Farmakis, D.2
Karagiorga, M.3
Voskaridou, E.4
Loutradi, A.5
Hatziliami, A.6
-
9
-
-
0036322256
-
Cardiac abnormalities in children with sickle cell anemia
-
Batra AS, Acherman RJ, Wong WY, Wood JC, Chan LS, Ramicone E, et al. Cardiac abnormalities in children with sickle cell anemia. Am J Hematol 2002;70:306-12.
-
(2002)
Am J Hematol
, vol.70
, pp. 306-312
-
-
Batra, A.S.1
Acherman, R.J.2
Wong, W.Y.3
Wood, J.C.4
Chan, L.S.5
Ramicone, E.6
-
10
-
-
33645065138
-
Myelodysplastic syndromes: Iron overload consequences and current chelating therapies
-
Greenberg PL. Myelodysplastic syndromes: iron overload consequences and current chelating therapies. J Natl Compr Canc Netw 2006;4:91-6.
-
(2006)
J Natl Compr Canc Netw
, vol.4
, pp. 91-96
-
-
Greenberg, P.L.1
-
12
-
-
0028059813
-
Efficacy of deferoxamine in preventing complications of iron overload in patients with thalassemia major
-
Brittenham GM, Griffith PM, Nienhuis AW, McLaren CE, Young NS, Tucker EE, et al. Efficacy of deferoxamine in preventing complications of iron overload in patients with thalassemia major. N Engl J Med 1994;331:567-73.
-
(1994)
N Engl J Med
, vol.331
, pp. 567-573
-
-
Brittenham, G.M.1
Griffith, P.M.2
Nienhuis, A.W.3
McLaren, C.E.4
Young, N.S.5
Tucker, E.E.6
-
13
-
-
0034631379
-
Survival in beta-thalassaemia major in the UK: Data from the UK Thalassaemia Register
-
Modell B, Khan M, Darlison M. Survival in beta-thalassaemia major in the UK: data from the UK Thalassaemia Register. Lancet 2000;355:2051-2.
-
(2000)
Lancet
, vol.355
, pp. 2051-2052
-
-
Modell, B.1
Khan, M.2
Darlison, M.3
-
14
-
-
0028086414
-
Survival in medically treated patients with homozygous beta-thalassemia
-
Olivieri NF, Nathan DG, MacMillan JH, Wayne AS, Liu PP, McGee A, et al. Survival in medically treated patients with homozygous beta-thalassemia. N Engl J Med 1994;331:574-8.
-
(1994)
N Engl J Med
, vol.331
, pp. 574-578
-
-
Olivieri, N.F.1
Nathan, D.G.2
Macmillan, J.H.3
Wayne, A.S.4
Liu, P.P.5
McGee, A.6
-
15
-
-
0032514558
-
Long-term safety and effectiveness of iron-chelation therapy with deferiprone for thalassemia major
-
Olivieri NF, Brittenham GM, McLaren CE, Templeton DM, Cameron RG, McClelland RA, et al. Long-term safety and effectiveness of iron-chelation therapy with deferiprone for thalassemia major. N Engl J Med 1998;339:417-23.
-
(1998)
N Engl J Med
, vol.339
, pp. 417-423
-
-
Olivieri, N.F.1
Brittenham, G.M.2
McLaren, C.E.3
Templeton, D.M.4
Cameron, R.G.5
McClelland, R.A.6
-
16
-
-
10744230223
-
Effectiveness and safety of ICL670 in iron-loaded patients with thalassaemia: A randomised, double-blind, placebo-controlled, dose-escalation trial
-
Nisbet-Brown E, Olivieri NF, Giardina PJ, Grady RW, Neufeld EJ, Sechaud R, et al. Effectiveness and safety of ICL670 in iron-loaded patients with thalassaemia: a randomised, double-blind, placebo-controlled, dose-escalation trial. Lancet 2003;361:1597-602.
-
(2003)
Lancet
, vol.361
, pp. 1597-1602
-
-
Nisbet-Brown, E.1
Olivieri, N.F.2
Giardina, P.J.3
Grady, R.W.4
Neufeld, E.J.5
Sechaud, R.6
-
17
-
-
33646414765
-
A phase 3 study of deferasirox (ICL670), a once-daily oral iron chelator, in patients with beta-thalassemia
-
Cappellini MD, Cohen A, Piga A, Bejaoui M, Perrotta S, Agaoglu L, et al. A phase 3 study of deferasirox (ICL670), a once-daily oral iron chelator, in patients with beta-thalassemia. Blood 2006;107:3455-62.
-
(2006)
Blood
, vol.107
, pp. 3455-3462
-
-
Cappellini, M.D.1
Cohen, A.2
Piga, A.3
Bejaoui, M.4
Perrotta, S.5
Agaoglu, L.6
-
18
-
-
33846012866
-
A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease
-
Vichinsky E, Onyekwere O, Porter J, Swerdlow P, Eckman J, Lane P, et al. A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease. Br J Haematol 2007;136:501-8.
-
(2007)
Br J Haematol
, vol.136
, pp. 501-508
-
-
Vichinsky, E.1
Onyekwere, O.2
Porter, J.3
Swerdlow, P.4
Eckman, J.5
Lane, P.6
-
19
-
-
65349152022
-
Efficacy and safety of deferasirox, an oral iron chelator, in heavily iron-overloaded patients with betathalassaemia: The ESCALATOR study
-
Taher A, El-Beshlawy A, Elalfy MS, Al Zir K, Daar S, Damanhouri G, et al. Efficacy and safety of deferasirox, an oral iron chelator, in heavily iron-overloaded patients with betathalassaemia: the ESCALATOR study. Eur J Haematol 2009;82:458-65.
-
(2009)
Eur J Haematol
, vol.82
, pp. 458-465
-
-
Taher, A.1
El-Beshlawy, A.2
Elalfy, M.S.3
Al Zir, K.4
Daar, S.5
Damanhouri, G.6
-
20
-
-
0019952276
-
Proposals for the classification of the myelodysplastic syndromes
-
Bennett JM, Catovsky D, Daniel MT, Flandrin G, Galton DA, Gralnick HR, et al. Proposals for the classification of the myelodysplastic syndromes. Br J Haematol 1982;51:189-99.
-
(1982)
Br J Haematol
, vol.51
, pp. 189-199
-
-
Bennett, J.M.1
Catovsky, D.2
Daniel, M.T.3
Flandrin, G.4
Galton, D.A.5
Gralnick, H.R.6
-
21
-
-
0030897009
-
International scoring system for evaluating prognosis in myelodysplastic syndromes
-
Greenberg P, Cox C, LeBeau MM, Fenaux P, Morel P, Sanz G, et al. International scoring system for evaluating prognosis in myelodysplastic syndromes. Blood 1997;89:2079-88.
-
(1997)
Blood
, vol.89
, pp. 2079-2088
-
-
Greenberg, P.1
Cox, C.2
Lebeau, M.M.3
Fenaux, P.4
Morel, P.5
Sanz, G.6
-
22
-
-
0034601375
-
Hepatic iron concentration and total body iron stores in thalassemia major
-
Angelucci E, Brittenham GM, McLaren CE, Ripalti M, Baronciani D, Giardini C, et al. Hepatic iron concentration and total body iron stores in thalassemia major. N Engl J Med 2000;343:327-31.
-
(2000)
N Engl J Med
, vol.343
, pp. 327-331
-
-
Angelucci, E.1
Brittenham, G.M.2
McLaren, C.E.3
Ripalti, M.4
Baronciani, D.5
Giardini, C.6
-
23
-
-
0030588405
-
-
Iron overload disorders among Hispanics-San Diego, CA, USA, 1995
-
Iron overload disorders among Hispanics-San Diego, CA, USA, 1995. MMWR Morb Mortal Wkly Rep 1996;45:991-3.
-
(1996)
MMWR Morb Mortal Wkly Rep
, vol.45
, pp. 991-993
-
-
-
24
-
-
64949196097
-
Management of transfusional iron overload in Latin America: Current outlook and expert panel recommendations
-
Araújo A, Drelichman G, Cançdo RD, Watman N, Magalhães SM, Duhalde M, et al. Management of transfusional iron overload in Latin America: current outlook and expert panel recommendations. Hematology 2009;14:22-32.
-
(2009)
Hematology
, vol.14
, pp. 22-32
-
-
Araújo, A.1
Drelichman, G.2
Cançdo, R.D.3
Watman, N.4
Magalhães, S.M.5
Duhalde, M.6
-
25
-
-
0034446757
-
Community genetics in Latin America: Challenges and perspectives
-
Penchaszadeh VB. Community genetics in Latin America: challenges and perspectives. Community Genet 2000;3:124-7.
-
(2000)
Community Genet
, vol.3
, pp. 124-127
-
-
Penchaszadeh, V.B.1
-
26
-
-
0031870210
-
Medical genetic services in Latin America: Report of a meeting of experts
-
[cited 2009 Oct 22], Available from
-
Penchaszadeh VB, Beiguelman B. Medical genetic services in Latin America: report of a meeting of experts. Rev Panam Salud Publica [document on the internet]. 1998, vol. 3, no. 6 [cited 2009 Oct 22]. p. 409-420. Available from: http://www.scielosp.org/scielo.php?script5sci_arttext&pid5S1020-49891998000600013&lng5en&nrm5iso
-
(1998)
Rev Panam Salud Publica [document on the Internet]
, vol.3
, Issue.6
, pp. 409-420
-
-
Penchaszadeh, V.B.1
Beiguelman, B.2
-
27
-
-
1842339882
-
Molecular characterization of b-thalassemia genes in an Argentine population
-
Roldan A, Gutierrez M, Cygler A, Bonduel M, Sciuccati G, Torres AF. Molecular characterization of b-thalassemia genes in an Argentine population. Am J Hematol 1997;54:179-82.
-
(1997)
Am J Hematol
, vol.54
, pp. 179-182
-
-
Roldan, A.1
Gutierrez, M.2
Cygler, A.3
Bonduel, M.4
Sciuccati, G.5
Torres, A.F.6
-
29
-
-
0033842989
-
Sickle cell anemia and b-globin gene cluster haplotypes in Colombia
-
Cuéllar-Ambrosi F, Mondragón MC, Gigueroa M, Préhu C, Galactéros F, Ruiz-Linares A. Sickle cell anemia and b-globin gene cluster haplotypes in Colombia. Hemoglobin 2000;24:221-5.
-
(2000)
Hemoglobin
, vol.24
, pp. 221-225
-
-
Cuéllar-Ambrosi, F.1
Mondragón, M.C.2
Gigueroa, M.3
Préhu, C.4
Galactéros, F.5
Ruiz-Linares, A.6
-
30
-
-
0032474692
-
Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography
-
Adams RJ, McKie VC, Hsu L, Files B, Vichinsky E, Pegelow C, et al. Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography. N Engl J Med 1998;339:5-11.
-
(1998)
N Engl J Med
, vol.339
, pp. 5-11
-
-
Adams, R.J.1
McKie, V.C.2
Hsu, L.3
Files, B.4
Vichinsky, E.5
Pegelow, C.6
-
31
-
-
29544444495
-
Discontinuing prophylactic transfusions used to prevent stroke in sickle cell disease
-
Adams RJ, Brambilla D. Discontinuing prophylactic transfusions used to prevent stroke in sickle cell disease. N Engl J Med 2005;353:2769-78.
-
(2005)
N Engl J Med
, vol.353
, pp. 2769-2778
-
-
Adams, R.J.1
Brambilla, D.2
-
32
-
-
0035137382
-
Iron overload is a determinant of morbidity and mortality in adult patients with sickle cell disease
-
Ballas SK. Iron overload is a determinant of morbidity and mortality in adult patients with sickle cell disease. Semin Hematol 2001;38:30-6.
-
(2001)
Semin Hematol
, vol.38
, pp. 30-36
-
-
Ballas, S.K.1
-
33
-
-
24344505753
-
Comparison of organ dysfunction in transfused patients with SCD or b Thalssemia
-
Vichinsky E, Butensky E, Fung E, Hudes M, Theil E, Ferrell L, et al. Comparison of organ dysfunction in transfused patients with SCD or b Thalssemia. Am J Hematol 2005;80:70-4.
-
(2005)
Am J Hematol
, vol.80
, pp. 70-74
-
-
Vichinsky, E.1
Butensky, E.2
Fung, E.3
Hudes, M.4
Theil, E.5
Ferrell, L.6
-
34
-
-
33750049951
-
Increased prevalence of iron-overload associated endocrinopathy in thalassaemia versus sickle-cell disease
-
Fung EB, Harmatz PR, Lee PD, Milet M, Bellevue R, Jeng MR, et al. Increased prevalence of iron-overload associated endocrinopathy in thalassaemia versus sickle-cell disease. Br J Haematol 2006;135:574-82.
-
(2006)
Br J Haematol
, vol.135
, pp. 574-582
-
-
Fung, E.B.1
Harmatz, P.R.2
Lee, P.D.3
Milet, M.4
Bellevue, R.5
Jeng, M.R.6
-
35
-
-
50849084793
-
Disparity in the management of iron overload between patients with sickle cell disease and thalassemia who received transfusions
-
Fung EB, Harmatz PR, Milet M, Balasa V, Ballas SK, Casella JF, et al. Disparity in the management of iron overload between patients with sickle cell disease and thalassemia who received transfusions. Transfusion 2008;48:1971-80.
-
(2008)
Transfusion
, vol.48
, pp. 1971-1980
-
-
Fung, E.B.1
Harmatz, P.R.2
Milet, M.3
Balasa, V.4
Ballas, S.K.5
Casella, J.F.6
-
36
-
-
73149083256
-
Early cardiac iron overload in children with transfusion-dependent anemias
-
Fernandes JL, Fabron A, Verissimo M. Early cardiac iron overload in children with transfusion-dependent anemias. Haematologica 2009;94:1776-7.
-
(2009)
Haematologica
, vol.94
, pp. 1776-1777
-
-
Fernandes, J.L.1
Fabron, A.2
Verissimo, M.3
-
37
-
-
0031006274
-
Growth, puberty and endocrine function in betathalassemia major
-
Low LC. Growth, puberty and endocrine function in betathalassemia major. J Pediatr Endocrinol Metabl 1997;10:175-84.
-
(1997)
J Pediatr Endocrinol Metabl
, vol.10
, pp. 175-184
-
-
Low, L.C.1
-
38
-
-
0033932447
-
Early onset of endocrine abnormalities in beta-thalssemia major in a developing country
-
Gulati R, Bhatia V, Argarwal SS. Early onset of endocrine abnormalities in beta-thalssemia major in a developing country. J Pediatr Endocrinol Metab 2000;13:651-6.
-
(2000)
J Pediatr Endocrinol Metab
, vol.13
, pp. 651-656
-
-
Gulati, R.1
Bhatia, V.2
Argarwal, S.S.3
-
39
-
-
0033046345
-
Growth and pubertal development in transfusion-dependent children and adolescents with thalassemia major and sickle cell disease: A comparative study
-
Soliman AT, el-Zalabany M, Amer M, Ansari BM. Growth and pubertal development in transfusion-dependent children and adolescents with thalassemia major and sickle cell disease: a comparative study. J Trop Pediatr 1999;4591:23-30.
-
(1999)
J Trop Pediatr
, vol.4591
, pp. 23-30
-
-
Soliman, A.T.1
El-Zalabany, M.2
Amer, M.3
Ansari, B.M.4
-
40
-
-
20844460608
-
Survival and complications in patients with thalassemia major treated with transfusion and deferoxamine
-
Borgna-Pignatti C, Rugolotto S, De Stefano P, Zhao H, Cappellini MD, Del Vecchio GC, et al. Survival and complications in patients with thalassemia major treated with transfusion and deferoxamine. Haematologica 2004;89:1187-93.
-
(2004)
Haematologica
, vol.89
, pp. 1187-1193
-
-
Borgna-Pignatti, C.1
Rugolotto, S.2
de Stefano, P.3
Zhao, H.4
Cappellini, M.D.5
del Vecchio, G.C.6
-
41
-
-
0034651775
-
Long-term outcome of continuous 24- hour deferoxamine infusion via indwelling intravenous catheters in high risk beta-thalassemia
-
Davis BA, Porter JB. Long-term outcome of continuous 24- hour deferoxamine infusion via indwelling intravenous catheters in high risk beta-thalassemia. Blood 2000;95:1229-36.
-
(2000)
Blood
, vol.95
, pp. 1229-1236
-
-
Davis, B.A.1
Porter, J.B.2
-
42
-
-
0030048681
-
Results of long-term iron-chelating therapy
-
Gabutti V, Piga A. Results of long-term iron-chelating therapy. Acta Haematol 1996;95:26-36.
-
(1996)
Acta Haematol
, vol.95
, pp. 26-36
-
-
Gabutti, V.1
Piga, A.2
-
43
-
-
73949153192
-
Serum ferritin level changes in children with sickle cell disease on chronic blood transfusions are non-linear, and are associated with iron load and liver injury
-
Adamkiewicz TV, Abboud MR, Paley C, Olivieri N, Kirby-Allen M, Vichinsky E, et al. Serum ferritin level changes in children with sickle cell disease on chronic blood transfusions are non-linear, and are associated with iron load and liver injury. Blood 2009;114:4632-8.
-
(2009)
Blood
, vol.114
, pp. 4632-4638
-
-
Adamkiewicz, T.V.1
Abboud, M.R.2
Paley, C.3
Olivieri, N.4
Kirby-Allen, M.5
Vichinsky, E.6
|