Lung disease in Niemann-Pick disease

Pediatric Pulmonology

Volumn 42, Issue 12, 2007, Pages 1207-1214

  Guillemot, Nathalie ^a   Troadec, Corinne ^a   De Villemeur, Thierry Billette ^a   Clément, Annick ^a   Fauroux, Brigitte ^a  

^a ARMAND TROUSSEAU HOSPITAL   (France)

Author keywords

Acid sphingomyelinase; Bronchoalveolar lavage; Children; Foamy macrophages; Interstitial lung disease

Indexed keywords

ARTICLE; CHILD; CHRONIC OBSTRUCTIVE LUNG DISEASE; CLINICAL ARTICLE; CLINICAL ASSESSMENT; CLINICAL EVALUATION; COMPUTER ASSISTED TOMOGRAPHY; CONTROLLED STUDY; FEMALE; FOAM CELL; FOAMY MACROPHAGE; HUMAN; INFANT; INTERSTITIAL LUNG DISEASE; INTERVENTION STUDY; LUNG DISEASE; LUNG FUNCTION TEST; LUNG LAVAGE; MALE; NIEMANN PICK DISEASE; OXYGEN THERAPY; PRIORITY JOURNAL; RESPIRATORY TRACT EXAMINATION; RETROSPECTIVE STUDY; RISK FACTOR; THORAX RADIOGRAPHY;

BIOPSY; BRONCHOALVEOLAR LAVAGE; BRONCHOALVEOLAR LAVAGE FLUID; CHILD; CHILD, PRESCHOOL; DIAGNOSIS, DIFFERENTIAL; FEMALE; HUMANS; INFANT; LUNG DISEASES, INTERSTITIAL; MALE; NIEMANN-PICK DISEASES; PROGNOSIS; RADIOGRAPHY, THORACIC; RESPIRATORY FUNCTION TESTS; SEVERITY OF ILLNESS INDEX;

EID: 36849014817     PISSN: 87556863     EISSN: 10990496     Source Type: Journal    
DOI: 10.1002/ppul.20725     Document Type: Article

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