Dyskeratosis congenita and the DNA damage response

British Journal of Haematology

Volumn 153, Issue 5, 2011, Pages 634-643

  Kirwan, Michael ^a   Beswick, Richard ^a   Walne, Amanda J ^a   Hossain, Upal ^a   Casimir, Colin ^b   Vulliamy, Tom ^a   Dokal, Inderjeet ^a  

^a QUEEN MARY UNIVERSITY OF LONDON   (United Kingdom)

^b MIDDLESEX UNIVERSITY   (United Kingdom)

Author keywords

Cell cycle; DNA damage; Dyskeratosis congenita; Lymphocytes; Telomeres

Indexed keywords

DNA; DYSKERIN; GAMMA HISTONE H2AX; HISTONE H2AX; NUCLEAR PROTEIN; PROTEIN 53BP1; PROTEIN P53; RNA; TELOMERASE REVERSE TRANSCRIPTASE; TELOMERASE RNA COMPONENT; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; APOPTOSIS; ARTICLE; CELL CYCLE ARREST; CELL TYPE; CHILD; CHROMOSOME DAMAGE; CLINICAL ARTICLE; CONCENTRATION RESPONSE; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DNA DAMAGE; DYSKERATOSIS CONGENITA; FEMALE; FIBROBLAST; FLOW CYTOMETRY; GENE MUTATION; GROWTH INHIBITION; HEMATOPOIETIC SYSTEM; HUMAN; HUMAN CELL; MALE; PHENOTYPE; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN INDUCTION; T LYMPHOCYTE; TELOMERE;

ADOLESCENT; ADULT; APOPTOSIS; CELL CYCLE; CHILD, PRESCHOOL; DNA DAMAGE; DYSKERATOSIS CONGENITA; FEMALE; FIBROBLASTS; HISTONES; HUMANS; INTRACELLULAR SIGNALING PEPTIDES AND PROTEINS; MALE; MICROSCOPY, CONFOCAL; T-LYMPHOCYTES; TELOMERE; TISSUE CULTURE TECHNIQUES; TUMOR SUPPRESSOR PROTEIN P53; UP-REGULATION; YOUNG ADULT;

EID: 79955708911     PISSN: 00071048     EISSN: 13652141     Source Type: Journal    
DOI: 10.1111/j.1365-2141.2011.08679.x     Document Type: Article

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