Secondary storage of dermatan sulfate in Sanfilippo disease

Journal of Biological Chemistry

Volumn 286, Issue 9, 2011, Pages 6955-6962

  Lamanna, William C ^a   Lawrence, Roger ^a   Sarrazin, Stéphane ^a   Esko, Jeffrey D ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CATABOLIC ENZYMES; CELL LINES; CENTRAL NERVOUS SYSTEMS; DERMAL FIBROBLASTS; DERMATAN SULFATE; ENZYME REPLACEMENT THERAPY; GLYCOSAMINOGLYCANS; HEPARAN SULFATES; INHERITED DISORDERS; LYSOSOMAL ENZYMES; SECONDARY METABOLITES; SECONDARY STORAGE; SULFATASES; SULFATE LEVELS; WILD TYPES;

BIOMOLECULES; CATALYSTS; CELL CULTURE; DIAGNOSIS; ENZYMES; FIBROBLASTS; METABOLITES;

METABOLISM;

CHONDROITIN; CHONDROITIN ABC LYASE; DERMATAN SULFATE; HEPARAN SULFATE; HEPARIN; IDURONATE 2 SULFATASE;

ARTICLE; CELL LINE; CONTROLLED STUDY; ENZYME INHIBITION; ENZYME REPLACEMENT; HUMAN; HUMAN CELL; LYSOSOME; METABOLITE; PRIORITY JOURNAL; SANFILIPPO SYNDROME; SKIN FIBROBLAST;

CELLS, CULTURED; CHONDROITIN SULFATES; DERMATAN SULFATE; ENZYME REPLACEMENT THERAPY; FIBROBLASTS; GLUCURONIDASE; HEPARITIN SULFATE; HUMANS; HYDROLASES; IDURONATE SULFATASE; LYSOSOMES; MUCOPOLYSACCHARIDOSIS III;

EID: 79953193429     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M110.192062     Document Type: Article

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